Norawat Rahul, Sarkar Deepa, Maybauer Marc O
Manchester Academic Health Science Centre, Cardiothoracic Anaesthesia and Intensive Care, Manchester University, Manchester University NHS Foundation Trust, Manchester, UK; Department of Cardiac Anaesthesia, Apollo Hospital, New Delhi, India.
Department of Cardiac Anaesthesia, Apollo Hospital, New Delhi, India.
Ann Card Anaesth. 2018 Oct-Dec;21(4):430-432. doi: 10.4103/aca.ACA_233_17.
Rhabdomyoma is the most common cardiac tumor in infancy and commonly located in the ventricles causing outflow obstruction or arrhythmias. We report a rare pediatric (7 month old) case of a right atrial rhabdomyoma presenting with severe cyanosis and low cardiac output from significant tricuspid inflow obstruction with right to left shunt across a stretched patent foramen ovale. We present an emergency cardiac surgery for right atrial tumor resection, and the management of separating the patient with failing right ventricle from cardiopulmonary bypass using a Glenn shunt, since extracorporeal membrane oxygenation (ECMO) or nitric oxide was not available.
横纹肌瘤是婴儿期最常见的心脏肿瘤，通常位于心室，可导致流出道梗阻或心律失常。我们报告一例罕见的儿科病例（7个月大），为右心房横纹肌瘤，因严重的三尖瓣流入道梗阻及经扩张的卵圆孔未闭的右向左分流，出现严重紫绀和低心输出量。我们进行了急诊心脏手术切除右心房肿瘤，并采用格林分流术将右心室功能衰竭的患者从体外循环中分离出来进行处理，因为当时无法使用体外膜肺氧合（ECMO）或一氧化氮。
