Tsuchiya Hiroko, Inagawa Gaku
Masui. 2017 Mar;66(3):320-321.
Erythropoietic protoporphyria (EPP) is a hereditary disease resulting from a deficiency in ferrochelatase required for haem synthesis system. We describe the anesthetic management of a 51-year-old man with EPP undergoing open reduction and internal fixation of patella fracture. Spinal anesthesia was induced with bupivacaine. The surgery was performed without any complications. No skin symptom was observed periop- eratively. Spinal anesthesia with bupivacaine can be safe for an EPP patient.
红细胞生成性原卟啉症(EPP)是一种由于血红素合成系统所需的铁螯合酶缺乏而导致的遗传性疾病。我们描述了一名51岁患有EPP的男性患者,在接受髌骨骨折切开复位内固定手术时的麻醉管理情况。使用布比卡因诱导蛛网膜下腔麻醉。手术过程顺利,无任何并发症。围手术期未观察到皮肤症状。对于EPP患者,使用布比卡因进行蛛网膜下腔麻醉可能是安全的。