Sharma Gopal, Jain Ayush, Sharma Prerit, Sharma Sonal, Rathi Vinita, Garg Pankaj Kumar
Department of Surgery, University College of Medical Sciences and Guru Teg Bahadur Hospital, University of Delhi, Delhi 110095, India.
Department of Pathology, University College of Medical Sciences and Guru Teg Bahadur Hospital, University of Delhi, Delhi 110095, India.
World J Clin Oncol. 2018 Nov 10;9(7):162-166. doi: 10.5306/wjco.v9.i7.162.
A 42-years-old lady, presented with a large retroperitoneal mass which was preoperatively diagnosed as a retroperitoneal liposarcoma following an image guided core biopsy. She underwent a margin-negative resection of the retroperitoneal mass (multi visceral resection - enbloc excision of the retroperitoneal mass with a left nephrectomy and a segmental descending colectomy). The final histopathological examination of the resected specimen confirmed an exophytic renal angiomyolipoma (AML) which was extending into the retroperitoneum. AML is a rare benign tumor arising most commonly from the kidney. It can sometimes present as a diagnostic challenge as it mimics a retroperitoneal liposarcoma or a fat-containing renal cell carcinomas closely. We present this case to share our experience of managing a case of giant exophytic AML which resembled retroperitoneal liposarcoma closely and resulted into an aggressive surgery.
一位42岁女性，因巨大腹膜后肿块就诊。在影像引导下进行穿刺活检后，术前诊断为腹膜后脂肪肉瘤。她接受了腹膜后肿块的切缘阴性切除术（多脏器切除——整块切除腹膜后肿块，同时切除左肾及部分降结肠）。切除标本的最终组织病理学检查证实为外生性肾血管平滑肌脂肪瘤（AML），该肿瘤已延伸至腹膜后。AML是一种罕见的良性肿瘤，最常见于肾脏。有时它会带来诊断挑战，因为它与腹膜后脂肪肉瘤或含脂肪的肾细胞癌极为相似。我们呈现此病例，以分享我们处理一例酷似腹膜后脂肪肉瘤的巨大外生性AML病例并导致进行根治性手术的经验。
