Alshehri Mohammed, Hakami Basel, Aljameel Nasser, Alayyaf Mohammad, Raheem Ali Abdel
Department of Urology, King Abdullah Bin AbdulAziz University Hospital, Princess Nourah Bint Abdulrahman University, Riyadh, Saudi Arabia.
Department of Urology, King Saud Medical City, Riyadh, Saudi Arabia.
Urol Ann. 2020 Apr-Jun;12(2):167-171. doi: 10.4103/UA.UA_26_19. Epub 2020 Apr 14.
Giant angiomyolipoma (AML) is uncommon benign renal neoplasm that occurs sporadic or in association with tuberous sclerosis syndrome. There is no specific cutoff tumor size and/or weight to define giant AMLs. Ovarian stimulation hormones might cause a marked increase in its size and subsequent bleeding risk. Incidental findings are not common in those patients as mass-associated symptoms always present. Computed tomography scan is the standard diagnostic imaging study except for tumors with poor fat content. According to the clinical presentation, site and side of renal involvement giant sporadic AMLs have different treatment options, for example, active surveillance, selective renal artery embolization, nephron-sparing surgery, and/or radical nephrectomy. In the present case report, we present a 22-year-old female with huge right renal mass (29 cm × 23 cm × 21 cm) and treated with right radical nephrectomy which proved to be renal AML on pathology examination.
巨大血管平滑肌脂肪瘤(AML)是一种罕见的良性肾肿瘤,可散发性发生或与结节性硬化综合征相关。目前尚无明确的肿瘤大小和/或重量标准来定义巨大AML。卵巢刺激激素可能会导致其大小显著增加,并随之增加出血风险。这些患者中偶然发现并不常见,因为总是会出现与肿块相关的症状。计算机断层扫描是标准的诊断性影像学检查,但脂肪含量低的肿瘤除外。根据临床表现、肾脏受累的部位和侧别,散发性巨大AML有不同的治疗选择,例如,主动监测、选择性肾动脉栓塞、保留肾单位手术和/或根治性肾切除术。在本病例报告中,我们介绍了一名22岁女性,其右肾有巨大肿块(29 cm×23 cm×21 cm),接受了右肾根治性切除术,术后病理检查证实为肾AML。