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未经治疗的钙化型小脑脂肪神经细胞瘤的临床病程。

Clinical course of the untreated calcified big cerebellar liponeurocytoma.

作者信息

Hamzaoglu Vural, Ozalp Hakan, Karatas Derya, Esen Kaan, Gurses Iclal, Dagtekin Ahmet, Avci Emel

机构信息

Mersin University School of Medicine, Department of Neurosurgery.

Mersin University School of Medicine, Department of Radiology.

出版信息

J Surg Case Rep. 2018 Nov 22;2018(11):rjy316. doi: 10.1093/jscr/rjy316. eCollection 2018 Nov.

DOI:10.1093/jscr/rjy316
PMID:30483397
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6249425/
Abstract

Cerebellar liponeurocytoma (CLN) is a very rare tumor of central nervous system, classified as glioneuronal tumor by the latest classification of World Health Organization (WHO) in 2016. There are limited data in the literature about biologic behavior, growth pattern and radiological features of this tumor. In this case report, we operated a big calcified CLN patient who had denied any surgical procedures suggested by an another institute and had been followed for 4 years.

摘要

小脑脂肪神经细胞瘤(CLN)是一种非常罕见的中枢神经系统肿瘤,在2016年世界卫生组织(WHO)的最新分类中被归类为神经胶质神经元肿瘤。关于这种肿瘤的生物学行为、生长模式和放射学特征,文献中的数据有限。在本病例报告中,我们为一名患有巨大钙化性CLN的患者进行了手术,该患者此前拒绝了另一家机构建议的任何手术治疗,并已接受了4年的随访。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/961d4c0a862f/rjy316f05.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/1b957ba2ac51/rjy316f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/11e977bba382/rjy316f02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/f5270df8aca0/rjy316f03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/eef0e6602e3c/rjy316f04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/961d4c0a862f/rjy316f05.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/1b957ba2ac51/rjy316f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/11e977bba382/rjy316f02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/f5270df8aca0/rjy316f03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/eef0e6602e3c/rjy316f04.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2684/6249425/961d4c0a862f/rjy316f05.jpg

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1
The 2016 World Health Organization Classification of Tumors of the Central Nervous System: a summary.2016 年世界卫生组织中枢神经系统肿瘤分类:概述。
Acta Neuropathol. 2016 Jun;131(6):803-20. doi: 10.1007/s00401-016-1545-1. Epub 2016 May 9.
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Cerebellar Liponeurocytoma, an Unusual Tumor of the Central Nervous System--Ultrastructural Examination.
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