Chaouche Ismail, El Bouardi Nizar, Benabderrazik Btissam, Haloua Meriem, Lamrani Moulay Youssef Alaoui, Boubbou Maryam, Maaroufi Mustapha, Alami Badreeddine
Diagnostic and Interventional Radiology Service, Hassan II Hospital Center, Route de Sefrou, Fes, Morocco.
Faculty of Medicine and Pharmacy of Fes, Sidi Mohammed Ben Abdallah University, Route d'Imouzzer, Fes, Morocco.
Radiol Case Rep. 2024 May 24;19(8):3382-3385. doi: 10.1016/j.radcr.2024.04.094. eCollection 2024 Aug.
Cerebellar liponeurocytoma is a rare WHO grade II glioneuronal tumor, characterized by a benign course and a more favorable prognosis. In this paper, we report a 52-year-old man, hospitalized in emergency because of clinical signs of increased intracranial pressure, and gait disturbances. The MRI revealed a lateral well shaped solid lesion within the left cerebellar hemisphere, having a low signal intensity compared to the cerebrospinal fluid, and causing a triventicular hydrocephalus and tonsillar herniation. The patient underwent a direct approach of the tumor through a left suboccipital craniectomy. Total removal of the lesion was achieved, and the histological diagnosis was cerebellar liponeurocytoma. The tumor cell proliferation index was < 6 %, therefore, radiotherapy and chemotherapy were not implemented after surgery. After 5 years of close follow-up there were no clinical or radiological signs of recurrence. Our objective in reporting another case of this unusual tumor is to discuss clinical profile, radiologic and histologic features as well as treatment and prognosis of this rare posterior fossa tumor.
小脑脂肪神经细胞瘤是一种罕见的世界卫生组织（WHO）Ⅱ级神经胶质神经元肿瘤，其特点是病程良性，预后较好。在本文中，我们报告了一名52岁男性，因颅内压升高的临床症状和步态障碍而急诊入院。磁共振成像（MRI）显示左小脑半球内有一个形态规则的外侧实性病变，与脑脊液相比信号强度较低，并导致三脑室脑积水和小脑扁桃体疝。患者通过左枕下颅骨切除术对肿瘤进行了直接手术入路。病变被完全切除，组织学诊断为小脑脂肪神经细胞瘤。肿瘤细胞增殖指数<6%，因此术后未进行放疗和化疗。经过5年的密切随访，没有复发的临床或影像学迹象。我们报告这例罕见肿瘤的目的是讨论这种罕见的后颅窝肿瘤的临床特征、放射学和组织学特征以及治疗和预后。
