Clara-Altamirano M A, García-Ortega D Y, Maciel-Miranda A, Martínez-Said H, Martínez-Tlahuel J L, Caro-Sánchez C H S, García-Ruíz G C, Cuellar-Hubbe M
Departamento de Piel y Partes Blandas del Instituto Nacional de Cancerología. Ciudad de México, México.
Ortopedia y Traumatología. Hospital Central «Dr. Ignacio Morones Prieto». México.
Acta Ortop Mex. 2018 May-Jun;32(3):167-171.
Dedifferentiated parosteal osteosarcoma is a variant in which a high grade osteosarcoma coexists with a parosteal osteosarcoma. We report the case of a 20-year-old female patient who presented with six months of evolution of pain and functional limitation of the right forearm, with no apparent cause; radiographs were performed, observing a tumoral lesion in the diaphysis of the right ulna. Physical examination showed pain upon palpation in the diaphysis of the ulna and limitation of prone-supination. Axial computed tomography of the thorax revealed metastatic disease in the upper lobe of the left lung. An incisional biopsy was performed on the right ulna, with a report of dedifferentiated parosteal osteosarcoma. Therefore, the patient was managed with neoadjuvant chemotherapy with cisplatin and doxorubicin until completing three cycles. Surgical treatment consisted of intercalary resection of the diaphysis of the right ulna, plus reconstruction of the microvascularized autologous graft of the right fibular diaphysis and graft stabilization with 3.5 mm dynamic compression plate (DCP) and one-third tubular plate. In the same procedure, pulmonary metastasectomy was performed by thoracoscopy. Post-surgical histopathological report with 100% necrosis. Currently, the patient is asymptomatic, with no evidence of tumor activity. Dedifferentiated parosteal osteosarcoma is a rare pathology, but should be suspected as a differential diagnosis in the presence of a parosteal osteosarcoma; it should be taken into account that this disease can metastasize due to its dedifferentiated pattern. It is important to plan a surgical treatment that allows an adequate functional reconstruction, always taking into account the oncological principle.
去分化骨旁骨肉瘤是一种高级别骨肉瘤与骨旁骨肉瘤共存的变异型。我们报告了一例20岁女性患者,其右前臂疼痛和功能受限6个月,无明显病因;进行了X线检查,发现右尺骨干有肿瘤病变。体格检查显示尺骨干触诊时有疼痛,旋前旋后受限。胸部轴向计算机断层扫描显示左肺上叶有转移性疾病。对右尺骨进行了切开活检,报告为去分化骨旁骨肉瘤。因此,患者接受了顺铂和阿霉素新辅助化疗,直至完成三个周期。手术治疗包括右尺骨干间置切除,加上右腓骨干带血管蒂自体移植重建及用3.5毫米动力加压钢板(DCP)和三分之一管状钢板固定移植骨。在同一手术中,通过胸腔镜进行了肺转移瘤切除术。术后组织病理学报告显示坏死率为100%。目前,患者无症状,无肿瘤活动迹象。去分化骨旁骨肉瘤是一种罕见的病理类型,但在存在骨旁骨肉瘤时应怀疑为鉴别诊断;应考虑到这种疾病因其去分化模式可能发生转移。规划一种能够进行充分功能重建的手术治疗方案很重要,同时始终要考虑肿瘤学原则。