Department of Clinical and Translational Medicine Dental School University of Rome "Tor Vergata", Rome, Italy.
Department of Surgical Sciences, Dental School, Catholic University of Our Lady of Good Counsel of Tirane, Tirane, Albania.
Eur J Paediatr Dent. 2018 Dec;19(4):303-306. doi: 10.23804/ejpd.2018.19.04.10.
Dentinogenesis imperfecta (DI) is an autosomal dominant genetic disease that affects both deciduous and permanent teeth, with an incidence of 1 out of 6,000 to 1 out of 8,000. Teeth affected with DI type II present bulbous crowns, short and constricted roots, marked cervical constriction, translucent enamel and amber dentin. Also, they present a partial or total obliteration of pulp space, due to continuous dentin production. SEM analysis has shown an undulated dentin-enamel junction (DEJ) with irregularities and locally wide spaces between the two structures instead of a strict junction and a regular linear surface. Treatment options for patients affected by DI-II are intended to protect and restore function and aesthetics of both posterior and anterior teeth. In literature are presented many different therapies, but mainly centered on cemented prosthetic restorations instead of adhesive restorative procedures. We present in this paper a DI-II case successfully treated in 2005 with extensive adhesive rehabilitation.
The 13 years follow-up proves the reliability of adhesion to dentine and enamel for indirect adhesive restorations even on this kind of anomalous substrates.
牙本质生成不全（DI）是一种常染色体显性遗传疾病，影响乳牙和恒牙，发病率为每 6000 至 8000 人中 1 例。患有 DI 型 II 的牙齿呈现球状冠、短而狭窄的根、明显的颈部收缩、半透明的釉质和琥珀色的牙本质。此外，由于持续的牙本质生成，牙髓腔会出现部分或完全闭塞。扫描电镜分析显示，牙釉质-牙本质交界处（DEJ）呈波浪状，两个结构之间不规则且局部有宽间隙，而不是严格的交界处和规则的线性表面。DI-II 患者的治疗选择旨在保护和恢复后牙和前牙的功能和美观。文献中提出了许多不同的治疗方法，但主要集中在粘固修复体上，而不是粘固修复程序。我们在本文中介绍了一个 DI-II 病例，该病例于 2005 年成功接受了广泛的粘固修复治疗。
13 年的随访证明了间接粘固修复对牙本质和牙釉质的粘固可靠性，即使在这种异常的底物上也是如此。
