Azzakhmam Mustapha, Zouaidia Fouad, Jahid Ahmed, Znati Kaoutar, Bernoussi Zakia, Mahassini Najat
Laboratoire d'Anatomie Pathologique, Hôpital Militaire d'Instruction Mohamed V, Rabat, Faculté de Médecine et de Pharmacie de Rabat, Maroc.
Laboratoire d'Anatomie Pathologique, Centre Hospitalier Universitaire Avicenne, Rabat, Maroc.
Pan Afr Med J. 2018 Jul 25;30:225. doi: 10.11604/pamj.2018.30.225.15484. eCollection 2018.
Pseudomyxoma peritonei (PMP) is a clinicopathologic syndrome characterized by mucinous ascites and pools of mucin resulting in neoplastic mucinous epithelium in the peritoneal cavity. PMP is uncommon and it is characterized by clinical and unusual pathologic manifestations posing diagnostic and therapeutic problems. Involvement of abdominal viscera and lymph node metastases are rare and sporadic cases have been reported in the literature. We here report the case of a 56-year old patient who had undergone two operations for PMP of appendicular origin presenting with progressive abdominal pain five years after his last treatment. Scanner objectified a recurrence of peritoneal pseudo-myxoma with liver and splenic intraparenchymatous lesions. Anatomopathological examination showed intrasplenic and hepatic recurrence of low-grade peritoneal pseudo-myxoma confirming the metastases.
腹膜假黏液瘤（PMP）是一种临床病理综合征，其特征为黏液性腹水和黏液池，导致腹腔内出现肿瘤性黏液上皮。PMP并不常见，具有临床和不寻常的病理表现，给诊断和治疗带来问题。腹部脏器受累和淋巴结转移很少见，文献中报道过散发病例。我们在此报告一例56岁患者，其因阑尾源性PMP接受了两次手术，在最后一次治疗五年后出现进行性腹痛。扫描显示腹膜假黏液瘤复发，并伴有肝实质内和脾实质内病变。解剖病理学检查显示低度腹膜假黏液瘤在脾内和肝内复发，证实了转移。
