Vicente Carla Sofia, Freitas António Dias
Centro Hospitalar Lisboa Central, Lisboa, Portugal.
Hospital de Cascais, Cascais, Portugal.
Pan Afr Med J. 2018 Jul 26;30:230. doi: 10.11604/pamj.2018.30.230.15950. eCollection 2018.
Behçet syndrome is a chronic, recurring, systemic disorder characterized by the histopathologic finding of nonspecific vasculitis in multiple organs. Behçet syndrome involves the gastrointestinal tract in 10-50% of patients; The main sites of involvement are the terminal ileum and cecum. In patients with Behçet syndrome, CT is advocated for early detection of complications as well as for exclusion of other abdominal pathologic conditions but there is no specific exam. The report of histology in conjunction with the clinical history and the presence of oral ulcers, uveitis and suspected cutaneous lesions suggests the diagnosis. The optimal medical treatment of Behçet syndrome has not yet been well established. In rare cases surgery must be required to control the disease. The authors report one case of Behcet Syndrome presenting with intestinal perforation.
白塞病是一种慢性、复发性全身性疾病，其特征是在多个器官出现非特异性血管炎的组织病理学表现。10%至50%的白塞病患者累及胃肠道；主要受累部位是回肠末端和盲肠。对于白塞病患者，提倡进行CT检查以早期发现并发症并排除其他腹部病理状况，但尚无特异性检查。结合临床病史以及口腔溃疡、葡萄膜炎和疑似皮肤病变进行组织学报告提示诊断。白塞病的最佳药物治疗方法尚未完全确立。在罕见情况下，必须进行手术以控制病情。作者报告了1例以肠穿孔为表现的白塞病病例。
