Starr Matthew R, Softing Hataye Alaina L, Bakri Sophie J
Department of Ophthalmology, Mayo Clinic, Rochester, Minnesota.
Retin Cases Brief Rep. 2021 Sep 1;15(5):500-503. doi: 10.1097/ICB.0000000000000849.
To describe a unique presentation of multifocal paracentral acute middle maculopathy in a young patient with juvenile dermatomyositis including optical coherence tomography angiography findings.
Retrospective single case report.
Seventeen-year-old male patient with a history of juvenile dermatomyositis presented for routine hydroxychloroquine screening.
Optical coherence tomography revealed undulations of the outer retinal layers and retinal thinning near the fovea in both eyes. Optical coherence tomography angiography revealed loss of flow void densities in the superficial and deep capillary plexi in both eyes. These findings were consistent with a diagnosis of paracentral acute middle maculopathy.
To the authors' knowledge, this is the first report of the optical coherence tomography angiography findings in paracentral acute middle maculopathy associated with juvenile dermatomyositis. The defects were located in the superficial and deep capillary plexi and likely due to the known occlusive retinopathy associated with juvenile dermatomyositis.
描述一名患有青少年皮肌炎的年轻患者多灶性中心旁急性黄斑病变的独特表现，包括光学相干断层扫描血管造影结果。
回顾性单病例报告。
一名17岁男性患者，有青少年皮肌炎病史，前来进行常规羟氯喹筛查。
光学相干断层扫描显示双眼视网膜外层有起伏，黄斑中心凹附近视网膜变薄。光学相干断层扫描血管造影显示双眼浅表和深层毛细血管丛血流信号密度缺失。这些发现符合中心旁急性黄斑病变的诊断。
据作者所知，这是第一份关于与青少年皮肌炎相关的中心旁急性黄斑病变的光学相干断层扫描血管造影结果的报告。病变位于浅表和深层毛细血管丛，可能是由于已知的与青少年皮肌炎相关的闭塞性视网膜病变所致。
