a Department of Ophthalmology and Visual Sciences, John A. Moran Eye Center , University of Utah , Salt Lake City , Utah , USA.
b Department of Pediatrics, Division of Pediatric Rheumatology , University of Utah , Salt Lake City , Utah , USA.
Ocul Immunol Inflamm. 2018;26(6):929-933. doi: 10.1080/09273948.2017.1305421. Epub 2017 Apr 27.
To review a case of bilateral diffuse chorioretinopathy as a presenting sign of juvenile dermatomyositis (JDM) and review the literature regarding retinal manifestations associated with this disease.
Review of case record and literature regarding retinal manifestations related to juvenile dermatomyositis.
A 13-year-old girl presented with bilateral diffuse chorioretinopathy as the presenting sign of juvenile dermatomyositis. A review of the literature suggests that retinopathy associated with JDM is a rare finding that is symptomatic to patients and often responds to systemic treatment of juvenile dermatomyositis. This is also the first documented case of paracentral acute middle maculopathy in the setting of juvenile dermatomyositis.
Chorioretinopathy is a rare finding in juvenile dermatomyositis. While all patients with JDM likely do not warrant screening ophthalmologic examinations, any patient who has visual symptoms should have a careful dilated examination to evaluate for retinopathy or steroid-induced cataracts.
回顾一例双侧弥漫性脉络膜视网膜炎作为幼年型皮肌炎（JDM）的首发表现，并复习与该疾病相关的视网膜表现的文献。
回顾与幼年型皮肌炎相关的视网膜表现的病例记录和文献。
一名 13 岁女孩以双侧弥漫性脉络膜视网膜炎为幼年型皮肌炎的首发表现。文献复习提示，与 JDM 相关的视网膜病变是一种罕见的表现，对患者有症状，且常对幼年型皮肌炎的全身治疗有反应。这也是在幼年型皮肌炎背景下首例记录到的旁中心性急性中黄斑病变。
脉络膜视网膜炎在幼年型皮肌炎中较为罕见。虽然并非所有 JDM 患者都需要进行眼科筛查检查，但任何有视觉症状的患者都应进行仔细的散瞳检查，以评估是否存在视网膜病变或类固醇诱导性白内障。
