Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Room no 318, Srishty building, SCTIMST Staff Quarters, Poondi Road, Kumarapuram Junction, Medical college (P.O), Trivandrum, Kerala, 695011, India.
Department of Neurosurgery, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, Kerala, 695011, India.
Acta Neurochir (Wien). 2019 Feb;161(2):355-359. doi: 10.1007/s00701-018-03795-z. Epub 2019 Jan 14.
A 13-year-old male child was evaluated for headache and visual deterioration; he underwent routine MRI imaging which revealed a large craniopharyngeal canal, divided by an abnormal bony septum giving a bipartite appearance of the canal, with a lipoma and cephalocele on either side of the septum. The child had undergone a previous surgery for cleft palate repair at the age of 7. The child had normal pituitary function inspite of nonvisualization of pituitary gland in MRI. To best our knowledge, this is the first case with such a variation. We have also discussed the possible embryological hypothesis for this previously unreported entity. Knowledge about this rare variant might have surgical relevance in selected cases.
一位 13 岁男性儿童因头痛和视力下降就诊,接受了常规 MRI 成像检查,结果显示颅咽管巨大,由异常骨隔分为两部分,隔的两侧分别有脂肪瘤和脑膜膨出。该儿童在 7 岁时曾因腭裂修复接受过一次手术。尽管 MRI 未显示垂体,但儿童的垂体功能正常。据我们所知,这是首例此类变异病例。我们还讨论了这种以前未报道过的实体的可能胚胎学假说。在某些情况下,了解这种罕见的变异可能具有手术相关性。