Yacoub Hussam A, Li P Mark, Bemporad Joshua A, Khaitov Dmitry, Brown Daniel F
a Departments of Medicine (Division of Neurology) , Lehigh Valley Health Network , Allentown , PA , USA.
b Surgery (Division of Neurological/Spine Surgery) , Lehigh Valley Health Network , Allentown , PA , USA.
Hosp Pract (1995). 2019 Apr;47(2):99-103. doi: 10.1080/21548331.2019.1575645. Epub 2019 Feb 6.
Hypertrophic pachymeningitis (HP) is a chronic, progressive diffuse inflammatory condition that leads to thickening of the dura mater and can be idiopathic or associated with sarcoidosis among other disorders. In this case report, we present a rare case of cervical spine HP in a 29-year-old woman in the post-partum period, who had a history of pituitary adenoma and juvenile rheumatoid arthritis. Magnetic resonance imaging (MRI) of the spine revealed a soft tissue mass and moderate cord compression. The patient underwent C3-C7 laminectomy. Pathological analysis of the cervical epidural mass demonstrated a reactive inflammatory cell process. Recurrence of symptoms and worsening of pachymeningitis on imaging studies warranted further work-up which revealed mediastinal/hilar lymphadenopathy. Transbronchial biopsy revealed non-caseating granulomatous disease consistent with sarcoidosis. The patient was started on oral steroids and eventually methotrexate with significant clinical and radiographic improvement. Follow-up imaging studies showed minimal dural thickening in the thoracic spine and eventually complete resolution. HP should be considered in a patient with spinal cord compression, myelopathy, and radicular pain of unclear etiology, and sarcoidosis should be considered in idiopathic cases.
肥厚性硬脑膜炎(HP)是一种慢性、进行性弥漫性炎症性疾病,可导致硬脑膜增厚,病因可为特发性,也可与结节病等其他疾病相关。在本病例报告中,我们介绍了一名产后29岁女性的罕见颈椎HP病例,该患者有垂体腺瘤和幼年类风湿关节炎病史。脊柱磁共振成像(MRI)显示有软组织肿块和中度脊髓受压。患者接受了C3 - C7椎板切除术。颈椎硬膜外肿块的病理分析显示为反应性炎症细胞过程。症状复发和影像学研究显示硬脑膜炎恶化,因此需要进一步检查,结果发现纵隔/肺门淋巴结肿大。经支气管活检显示为与结节病相符的非干酪性肉芽肿病。患者开始口服类固醇,最终使用甲氨蝶呤,临床和影像学均有显著改善。后续影像学研究显示胸椎硬脑膜增厚轻微,最终完全消退。对于病因不明的脊髓受压、脊髓病和神经根性疼痛患者,应考虑HP,对于特发性病例,应考虑结节病。