特发性肥厚性颈段硬脑膜炎：一例随访5年的病例报告

Idiopathic hypertrophic cervical pachymeningitis: a case report with 5 year follow up.

作者信息

Khadilkar S V, Menezes K, Parekh H N, Ursekar M, Bhagwati S N

机构信息

Department of Neurology, Grant Medical College and Sir JJ Group of Hospitals, Mumbai.

出版信息

J Assoc Physicians India. 2003 Apr;51:391-3.

PMID:12723656

Abstract

Idiopathic hypertrophic pachymeningitis is an extremely rare entity. It usually affects cranial meninges. The spinal form is further uncommon and presents as a chronic progressive disease. We describe a 42 year old female with isolated idiopathic hypertrophic cervical pachymeningitis who had a relapsing remitting course under observation for five years. Laminectomy and immunosuppressive therapy produced temporary and partial relief. The long term course and relevant literature is reviewed.

摘要

特发性肥厚性硬脑膜炎是一种极为罕见的疾病。它通常累及颅部脑膜。脊髓型更为少见，表现为慢性进行性疾病。我们描述了一名42岁女性，患有孤立性特发性肥厚性颈段硬脑膜炎，在观察的五年中呈复发缓解病程。椎板切除术和免疫抑制治疗产生了暂时和部分缓解。本文回顾了其长期病程及相关文献。