Wells T R, Gwinn J L, Landing B H, Stanley P
Department of Pathology, Childrens Hospital of Los Angeles, CA 90027.
J Pediatr Surg. 1988 Oct;23(10):892-8. doi: 10.1016/s0022-3468(88)80379-8.
In sling (retrotracheal) left pulmonary artery (SLPA), the tracheobronchial pattern is generally considered basically normal. Analysis of dissected specimens and/or bronchograms and other preparations from five studied and 32 reported patients suggests that there are two different forms of SLPA: (1) types 1A and B, with normal TB pattern [with (A) or without (B) a right pre-eparterial (tracheal bronchus)], and the aberrant left pulmonary artery causing TB compression. The tracheal bifurcation in type 1 SLPA is usually demonstrable at the fourth to fifth thoracic vertebral level; (2A) SLPA type 2A, with bridging bronchus (BB), in which condition the right main bronchus supplies the right upper lobe, but the bronchus supplying the right middle and lower lobes (the bridging bronchus) arises from the left main bronchus (LMB), posterior to which the SLPA courses; (2B) SLPA type 2B, with absence of the right bronchial tree, and the right lung (usually hypoplastic) supplied by a BB from the LMB, posterior to which the SLPA courses. SLPA types 2A and B have in common varying degrees of tracheal stenosis with abnormal cartilage rings and absent tracheal pars membranacea, abnormally low tracheal "bifurcation" (pseudocarina) at average level T6, increased bronchial angles with "inverted T" pattern, and lower level of anterior esophageal indentation by the SLPA than SLPA type 1. Imperforate anus occurred in 8/58 (14%) of patients with SLPA types 2A or B, but possibly in none with SLPA type 1. SLPA type 2 is the predominant form of SLPA, with the incidence of type 2B being twice that of type 2A.(ABSTRACT TRUNCATED AT 250 WORDS)
在吊带型(气管后)左肺动脉(SLPA)中,气管支气管形态通常被认为基本正常。对5例研究病例和32例报告病例的解剖标本、支气管造影及其他标本分析表明,SLPA有两种不同形式:(1)1A和B型,气管支气管形态正常[(A)型有右动脉前(气管支气管),(B)型无],异常左肺动脉导致气管支气管受压。1型SLPA的气管分叉通常在胸4至胸5椎体水平可见;(2A)2A型SLPA,有桥接支气管(BB),在此情况下,右主支气管供应右上叶,但供应右中、下叶的支气管(桥接支气管)起自左主支气管(LMB),SLPA在其后方走行;(2B)2B型SLPA,无右支气管树,右肺(通常发育不全)由LMB发出的BB供应,SLPA在其后方走行。2A和2B型SLPA的共同特点是有不同程度的气管狭窄,软骨环异常且气管膜部缺如,气管“分叉”(假隆突)异常低,平均在胸6水平,支气管角增大呈“倒T”形,且SLPA导致的食管前方压迹水平低于1型SLPA。肛门闭锁发生在2A或2B型SLPA患者的8/58(14%)中,但1型SLPA患者可能无此情况。2型SLPA是SLPA的主要形式,2B型的发生率是2A型的两倍。(摘要截断于250字)