M'Rad S, Le Thi Huong D u, Wechsler B, Monsigny M, Buthiau D, Colchen A, Godeau P
Service de Médecine interne, Groupe hospitalier Pitié-Salpétrière, Paris.
Rev Pneumol Clin. 1988;44(6):260-5.
We report a new case of localized primary tracheobronchial amyloidosis revealed by haemoptysis and effort dyspnea. The CT scan image was a homogeneous and circumferential thickening of the bronchial wall measuring 282 on the Hounsfield scale. At magnetic resonance imaging the amyloid substance was a slightly less intense than fat tissue in T1 and T2-weighted sequences. Treatment using Yag laser photoresection stabilized the lesions with one year follow-up. The review of the literature enables us to summarize the clinical, endoscopic, morphological, prognostic and therapeutic features of tracheobronchial amyloidosis, as well as pathogenic hypotheses and relationship with tracheobronchopathia osteoplastica.
我们报告了一例以咯血和劳力性呼吸困难为表现的局限性原发性气管支气管淀粉样变性新病例。CT扫描图像显示支气管壁均匀环形增厚，在Hounsfield密度计上测量值为282。在磁共振成像中，淀粉样物质在T1和T2加权序列中比脂肪组织的信号强度略低。使用钇铝石榴石激光光切除术进行治疗，经过一年的随访，病变得到稳定。文献回顾使我们能够总结气管支气管淀粉样变性的临床、内镜、形态学、预后和治疗特征，以及发病机制假说和与骨质化气管支气管病的关系。
