Olivares L M, Gatti J C, Romorini A, Chwojnik A, Cardama J E, Pizarielo G E
Facultad de Medicina, Universidad del Salvador, Buenos Aires.
Med Cutan Ibero Lat Am. 1988;16(6):481-8.
It has been analyzed seven patients, five females and two males, affected by progressive systemic sclerosis. Their ages range from 35 to 60 years. Three of them correspond to the CREST syndrome named variant. There were made: physical examination, electrocardiogram, echocardiogram and radionuclide techniques such as: Thallium perfusion (T201) and ventriculography (Tc99). The cardiac examination of all the patients showed: Left myocardiopathy in six patients, as well right myocardiopathy in two of them. Four patients were affected by chronic cor pulmonale, due to pulmonary hypertension. All the patients had developed diffuse thallium perfusion defects as well, having abnormal resting left ventricular function in three patients and function abnormality from right ventricle in two patients. It is necessary to point out the importance of making such study systematically, even in the case cardiac symptoms absence.
对7例进行性系统性硬化症患者进行了分析,其中5例女性,2例男性。他们的年龄在35至60岁之间。其中3例符合CREST综合征的变异型。进行了体格检查、心电图、超声心动图以及放射性核素技术检查,如铊灌注(T201)和心室造影(Tc99)。所有患者的心脏检查结果显示:6例患者存在左心肌病,其中2例还存在右心肌病。4例患者因肺动脉高压患有慢性肺源性心脏病。所有患者还出现了弥漫性铊灌注缺损,3例患者静息左心室功能异常,2例患者右心室功能异常。有必要指出,即使在没有心脏症状的情况下,系统地进行此类研究也很重要。