侵袭视神经结构的脊索样胶质瘤。

Chordoid Glioma Infiltrating Optic Structures.

机构信息

Sorbonne Universités (NS, ABS), UPMC Université Paris 06, UMR S968, Paris, France; Institut de la Vision (NS, ABS), Paris, France; Department of Clinical Neurosciences (NS, ABS), Geneva University School of Medicine, Geneva, Switzerland; Radiology Department (CNM), Hôpital Foch, Suresnes, France; Cytology and Pathology Department (MB), Hôpital Foch, Suresnes, France; and Neurosurgery Department (SA), Hôpital Foch, Suresnes, France.

出版信息

J Neuroophthalmol. 2019 Sep;39(3):408-410. doi: 10.1097/WNO.0000000000000757.

DOI:10.1097/WNO.0000000000000757

PMID:30829943

Abstract

Chordoid glioma of the third ventricle (CGTV) is a rare, slow-growing, World Health Organization Grade II glial tumor, with stereotyped localization in the anterior third ventricle. Despite being considered a noninvasive tumor, CGTV is usually associated with a poor clinical outcome due to its close proximity to important cerebral structures, such as the hypothalamus and visual pathways. Our patient with CGTV experienced visual involvement, but after subtotal surgical resection showed no evidence of progression at 5-year follow-up.

摘要

第三脑室脊索样胶质瘤（CGTV）是一种罕见的、生长缓慢的、世界卫生组织分级为 II 级的神经胶质瘤，其特征性定位于前第三脑室。尽管 CGTV 被认为是一种非侵袭性肿瘤，但由于其紧邻下丘脑和视觉通路等重要脑结构，通常与不良的临床预后相关。我们的 CGTV 患者出现了视力受累，但在接受次全切除手术后 5 年的随访中没有发现进展的证据。