Isowa Masahide, Ueda Satoshi, Sonobe Makoto, Date Hiroshi
Department of Thoracic Surgery, Kyoto University Hospital, Kyoto, Japan.
Interact Cardiovasc Thorac Surg. 2019 Jul 1;29(1):154-156. doi: 10.1093/icvts/ivz032.
This is a case of type 1 congenital pulmonary airway malformation in the left lower lobe of a 26-year-old male. At the age of 1 year, he developed a pulmonary cystic lesion, which was considered to be bronchopulmonary sequestration. He grew up healthy and showed no impairment during exercise; however, giant bullous lesion development along with compressed left upper lobe and mediastinum was recently noted; consequently, the patient was referred to our hospital for further examination. We diagnosed congenital pulmonary airway malformation and performed left lower lobectomy. Postoperative course was uneventful, but a restrictive change on pulmonary function test did not improve. This unusual course of congenital pulmonary airway malformation with bullous changes suggests the importance of early-stage resection.
这是一例26岁男性左下叶1型先天性肺气道畸形的病例。1岁时，他出现了一个肺囊性病变，当时被认为是支气管肺隔离症。他健康成长，运动时无功能损害；然而，最近发现出现了巨大肺大疱病变，同时左上叶和纵隔受压；因此，该患者被转诊至我院进一步检查。我们诊断为先天性肺气道畸形并实施了左下叶切除术。术后过程顺利，但肺功能测试中的限制性改变并未改善。这种伴有肺大疱改变的先天性肺气道畸形的不寻常病程提示了早期切除的重要性。
