Sanger Terence D, Ferman Diana
Division of Neurology Children's Hospital Los Angeles Los Angeles California USA.
Mov Disord Clin Pract. 2017 Sep 14;4(6):870-874. doi: 10.1002/mdc3.12533. eCollection 2017 Nov-Dec.
Abnormal involuntary postures are characteristic of dystonia, but the specific postures observed clinically have not previously been categorized or enumerated. The objective of this study was to determine whether there is a set of specific postures that are common between different children with dystonia.
Videotapes were examined from all children who were seen in a pediatric movement disorders clinic over a 4-year period and had a diagnosis of nonpsychogenic dystonia. In total, 179 children were included in the video review.
Visually similar postures were identified in 152 different children. Seven different common postures were identified. All 152 children exhibited at least 1 of these postures, and most had more than 1.
Involuntary postures in childhood dystonia exhibit unexpected similarities despite a wide range of underlying etiology, severity, and developmental experience. This is consistent with the hypothesis that childhood dystonia is a symptom that reflects a shared pathway of expression for multiple anatomic and functional abnormalities.
异常的不自主姿势是肌张力障碍的特征,但临床上观察到的具体姿势此前尚未进行分类或列举。本研究的目的是确定不同的肌张力障碍儿童之间是否存在一组共同的特定姿势。
对一家儿科运动障碍诊所4年间诊治的所有诊断为非精神源性肌张力障碍的儿童的录像进行检查。视频回顾共纳入179名儿童。
在152名不同儿童中发现了视觉上相似的姿势。确定了7种不同的常见姿势。所有152名儿童均表现出至少1种这些姿势,且大多数儿童有不止1种。
尽管存在广泛的潜在病因、严重程度和发育经历,但儿童肌张力障碍中的不自主姿势表现出意想不到的相似性。这与儿童肌张力障碍是一种反映多种解剖和功能异常共同表达途径的症状这一假设一致。