对仅存的单侧肺进行单灶化完全修复。
Complete repair with unifocalization of the only unilateral lung.
作者信息
Ishidou Motonori, Ota Keisuke, Kanno Kazuyoshi, Murata Masaya, Hirose Keiichi, Nagato Hisao, Sakamoto Kisaburo, Ikai Akio
机构信息
Department of Cardiovascular Surgery, Mt. Fuji Shizuoka Children's Hospital, Urushiyama 860, Aoi-ku, Shizuoka, Shizuoka, 420-8660, Japan.
出版信息
Gen Thorac Cardiovasc Surg. 2020 May;68(5):538-541. doi: 10.1007/s11748-019-01109-3. Epub 2019 Mar 14.
A boy with 22q11.2 deletion was diagnosed with pulmonary atresia with ventricular septal defect (PAVSD) and major aortopulmonary collateral arteries (MAPCAs). At 8 months, unifocalization of left MAPCAs and BT shunt was performed at another hospital. However, they occluded directly after surgery. An angiography revealed 2 MAPCAs supplying all segments of the right lung. Qp:Qs was 2.24. At 1 year 6 months, we performed VSD closure with unifocalization of the only right lung vascularity, using intraoperative PA flow study. We report a successful case of complete repair with unilateral lung in PAVSD and MAPCAs.
一名患有22q11.2缺失的男孩被诊断为肺动脉闭锁合并室间隔缺损（PAVSD）及主要的体肺侧支动脉（MAPCAs）。8个月大时，在另一家医院进行了左MAPCAs的单源化和体肺分流术。然而，术后分流直接闭塞。血管造影显示有2条MAPCAs供应右肺的所有节段。肺循环血流量与体循环血流量之比（Qp:Qs）为2.24。1岁6个月时，我们利用术中肺动脉血流研究，进行了室间隔缺损修补术，并对仅有的右肺血管进行了单源化。我们报告了一例成功完成PAVSD和MAPCAs单侧肺完全修复的病例。
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