Uno Yoshimasa, Shinohara Gen, Nakao Mitsutaka, Morita Kiyozo
Department of Cardiac Surgery, The Jikei University School of Medicine, Tokyo, Japan.
Kyobu Geka. 2019 Mar;72(3):199-203.
We report a new-born case of total conus defect type ventricular septal defect (VSD) and single coronary artery with situs inversus totalis, suspected Kartagener syndrome clinically. After the birth, as the patient had suffered from respiratory distress due to high pulmonary blood flow through the large defect, surgery was planned at age of 14-days after birth. Under median sternotomy and cardiac arrest, patch closure of VSD was performed as ordinary fashion. In spite of the situs inversus totalis and single coronary artery arose from right coronary sinus, operator could have completed all of surgical procedure at the right side of patient as usual. No remarkable respiratory complication was seen postoperatively and she was discharged from hospital 18th day in a good condition.
我们报告1例患有完全性圆锥部缺损型室间隔缺损（VSD）及单支冠状动脉且全内脏转位的新生儿病例，临床怀疑患有卡塔格内综合征。出生后，由于巨大缺损导致肺血流量高，患者出现呼吸窘迫，计划在出生后14天进行手术。在正中胸骨切开术及心脏停搏下，按常规方式对VSD进行了补片修补。尽管存在全内脏转位且单支冠状动脉起源于右冠状动脉窦，但术者仍能像往常一样在患者右侧完成所有手术操作。术后未见明显呼吸并发症，她于第18天康复出院。
