Division of Cardiothoracic Surgery, Department of Surgery, Baylor College of Medicine, Houston, Texas.
Department of Cardiovascular Surgery, Texas Heart Institute, Houston, Texas.
Tex Heart Inst J. 2021 Jan 1;48(1). doi: 10.14503/THIJ-19-7112.
Kartagener syndrome is characterized by situs inversus and defective cilia motion, the latter of which can lead to chronic infections and respiratory failure. If lung transplant is indicated, dextrocardia can pose surgical challenges. We report a rare case of sequential bilateral lung transplant in a 58-year-old man with Kartagener syndrome whose left pulmonary artery was abnormal in length, location, and direction. After placing the donor lungs in their orthotopic position, we augmented the recipient left pulmonary artery with a bovine pericardial patch. After 17 months of follow-up, the patient was in good condition with excellent graft function.
卡塔格内综合征的特征是内脏反位和纤毛运动缺陷，后者可导致慢性感染和呼吸衰竭。如果需要进行肺移植，右位心会带来手术挑战。我们报告了 1 例卡塔格内综合征 58 岁男性患者的序贯双侧肺移植，该患者的左肺动脉长度、位置和方向异常。在将供肺置于原位后，我们使用牛心包补片增强了受体的左肺动脉。随访 17 个月后，患者情况良好，移植物功能良好。
