Noblet D, Rey C, Brévière G M, Marçon F, Pernot C, Dupuis C
Arch Mal Coeur Vaiss. 1986 May;79(5):649-57.
Fourteen cases of the congenital subclavian steal syndrome are presented with a review of 99 cases in the literature. This abnormality is usually asymptomatic and a fortuitous finding (clinical: asymmetric blood pressure; radiological: investigation of an associated cardiovascular malformation). The possible malformations are numerous and may be diagnosed by angiography: however, they can be suspected from three simple investigations, clinical examination indicating the side of lower blood pressure, chest X-ray and barium swallow. Seventy one per cent congenital subclavian steal syndromes are associated with a right-sided aortic arch, the steal being then almost always left-sided via a left subclavian artery anomaly. In this group, a left subclavian artery isolated from the aorta represents about a half of the cases. A cardiac malformation is present in one out of two cases and a patent ductus arteriosus uniting the left subclavian artery and the left pulmonary artery is observed in one out of four cases. Twenty nine per cent of congenital subclavian steal syndromes are associated with a left-sided aortic arch. In these cases the abnormalities usually involve the aortic arch (57% of cases) or a right or left subclavian artery. Therefore, in this group, there is no preferential side for the subclavian steal which can be right, left or bilateral. These abnormalities usually only require medical surveillance. When they become symptomatic, vertebro-subclavian revascularisation is justified. The presence of a subclavian steal may have surgical implications: it is important to exclude a subclavian steal before performing a Blalock anastomosis.(ABSTRACT TRUNCATED AT 250 WORDS)
本文报告了14例先天性锁骨下动脉盗血综合征病例,并回顾了文献中的99例病例。这种异常通常无症状,多为偶然发现(临床:血压不对称;放射学:相关心血管畸形检查)。可能的畸形种类繁多,可通过血管造影诊断:然而,也可通过三项简单检查怀疑,临床检查可提示血压较低的一侧,胸部X线和吞钡检查。71%的先天性锁骨下动脉盗血综合征与右侧主动脉弓相关,盗血几乎总是通过左侧锁骨下动脉异常发生在左侧。在这组病例中,与主动脉分离的左侧锁骨下动脉约占一半。每两例中有一例存在心脏畸形,每四例中有一例观察到左锁骨下动脉与左肺动脉之间存在动脉导管未闭。29%的先天性锁骨下动脉盗血综合征与左侧主动脉弓相关。在这些病例中,异常通常累及主动脉弓(57%的病例)或右侧或左侧锁骨下动脉。因此,在这组病例中,锁骨下动脉盗血没有优先发生的一侧,可为右侧、左侧或双侧。这些异常通常仅需医学监测。当出现症状时,椎动脉-锁骨下动脉血管重建是合理的。锁骨下动脉盗血的存在可能具有手术意义:在进行Blalock吻合术之前排除锁骨下动脉盗血很重要。(摘要截选至250字)