Kumari Kalpana, Thota Ramya, Chaudhary Heera Lal, Sharma Mehar C, Thakar Alok, Singh Geetika
Department of Pathology, All India Institute of Medical Sciences, New Delhi, India.
Department of Otorhinolaryngology, All India Institute of Medical Sciences, New Delhi, India.
Head Neck Pathol. 2020 Mar;14(1):276-282. doi: 10.1007/s12105-019-01030-4. Epub 2019 Apr 4.
Low-grade fibromyxoid sarcoma (LGFMS) is an enigmatic soft tissue tumor. It frequently presents as a deeply seated mass in the proximal extremities and trunk. Superficial LGFMSs of the head and neck are exceedingly rare. Hyalinizing spindle cell tumor with giant rosettes (HSTGR) is an entity considered to be on the histologic spectrum of LGFMS. We present a case of a 44-year-old female who presented with a superficial, polypoid mass of the external auditory meatus. Microscopic examination revealed the classic histologic features of HSTGR. To our knowledge, this case is the first described at this extremely unusual location. Identification and reporting of such unusual cases is important to understand and compare the behavior of superficial LGFMS to that of the more common deeply seated tumors.
低度纤维黏液样肉瘤（LGFMS）是一种难以捉摸的软组织肿瘤。它常表现为近端肢体和躯干深处的肿块。头颈部的浅表LGFMS极为罕见。伴有巨大玫瑰花结的透明变性梭形细胞瘤（HSTGR）被认为是LGFMS组织学谱系中的一种病变。我们报告一例44岁女性，其外耳道出现浅表息肉样肿块。显微镜检查显示出HSTGR的典型组织学特征。据我们所知，该病例是首次报道于这一极其不寻常的部位。识别和报告此类不寻常病例对于理解和比较浅表LGFMS与更常见的深部肿瘤的行为很重要。
