The Affiliated Hospital of Zunyi Medical University, Zunyi, China.
The Third Affiliated Hospital of Zunyi Medical University, Zunyi, China.
BMC Musculoskelet Disord. 2019 Apr 9;20(1):154. doi: 10.1186/s12891-019-2542-z.
Gorham-Stout syndrome (GSS) with spinal involvement is extremely rare, and bilateral chylothorax as a complication is usually fatal. In our case, pleural effusion appeared in the left hemithorax after ligating the right thoracic duct.
A 14-year-old patient presented with GSS affecting the thoracic spine with bilateral chylothorax. The case was successfully managed using combined conservative and surgical treatments. At the 2-year follow-up visit, the amount of pleural fluid was reduced, the patient's respiratory function had improved, and the deformity on the thoracic spine had gradually stabilized.
GSS is a rare disorder of the musculoskeletal system that responds poorly to therapies and exhibits very high morbidity and mortality. Chylothorax is a common complication when lesions involve the thoracic spine, and physicians should be vigilant for possible serious pulmonary complications.
伴有脊柱受累的 Gorham-Stout 综合征（GSS）极为罕见，作为并发症的双侧乳糜胸通常是致命的。在我们的病例中，在结扎右侧胸导管后，左侧胸腔出现胸腔积液。
一名 14 岁患者因双侧乳糜胸而患有胸段脊柱 GSS。该病例通过联合保守和手术治疗成功得到控制。在 2 年的随访中，胸腔积液量减少，患者的呼吸功能得到改善，胸椎的畸形逐渐稳定。
GSS 是一种罕见的骨骼肌肉系统疾病，对治疗反应不佳，发病率和死亡率极高。当病变累及胸椎时，乳糜胸是一种常见的并发症，医生应警惕可能出现的严重肺部并发症。
