Kim Bong Jun, Kim Tae Hoon, Kim Do Jung, Noh Dongsub, Ham Seok Jin, Lee Sungsoo
Department of Thoracic and Cardiovascular Surgery, Gangnam Severance Hospital, Yonsei University College of Medicine.
Korean J Thorac Cardiovasc Surg. 2015 Feb;48(1):90-4. doi: 10.5090/kjtcs.2015.48.1.90. Epub 2015 Feb 5.
Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.
戈勒姆-斯托特综合征（GSS）是一种以局限性骨质吸收为特征的罕见疾病。骨骼的任何部位都可能受累；因此，症状可能因受累部位而异。病理分析显示，受累病变处有淋巴管增生和骨质溶解，但该疾病的病因尚不清楚。当GSS发生在胸部时，可能会出现乳糜胸或呼吸衰竭。迄今为止，尚未确立GSS的标准治疗方法，预后仍然未知。以下病例报告描述了一名16岁患有胸骨和肋骨受累的男孩GSS的成功治疗案例。
