Choi Taesoo, Yoo Koo Han, Song Ran, Lee Dong-Gi
Department of Urology, School of Medicine, Kyung Hee University, Seoul 05278, South Korea.
Division of Rheumatology, Department of Internal Medicine, School of Medicine, Kyung Hee University, Seoul 05278, South Korea.
World J Clin Cases. 2019 Mar 26;7(6):773-777. doi: 10.12998/wjcc.v7.i6.773.
Crossed fused renal ectopia is a rare congenital anomaly of the ascent of the kidney. This anomaly may be observed as a solitary kidney during initial evaluation. A solitary kidney must be evaluated for associated anomalies such as duplication, horseshoe kidney, or crossed renal ectopia.
An anomaly was observed in a 9-mo-old male child who was subsequently diagnosed with crossed fused renal ectopia and vesicoureteral reflux (VUR). In this condition, recurrent febrile urinary tract infection can be a serious problem, and can easily cause renal damage due to relatively short ureters and high pressure in the kidney.
To prevent urosepsis and preserve renal function, early diagnosis and proper management including surgical correction should be considered for the management of renal ectopia with VUR.
交叉融合性肾异位是一种罕见的肾脏上升先天性异常。在初始评估时,这种异常可能表现为孤立肾。对于孤立肾,必须评估是否存在相关异常,如重复肾、马蹄肾或交叉肾异位。
在一名9个月大的男童中观察到一种异常,该男童随后被诊断为交叉融合性肾异位和膀胱输尿管反流(VUR)。在这种情况下,复发性发热性尿路感染可能是一个严重问题,并且由于输尿管相对较短和肾脏内压力较高,很容易导致肾损伤。
为预防尿脓毒症并保留肾功能,对于合并VUR的肾异位的管理,应考虑早期诊断和包括手术矫正在内的适当管理。