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拉姆齐·亨特综合征伴真性声带麻痹——病例报告

Ramsay Hunt Syndrome Associated with True Vocal Cord Palsy- A Case Report.

作者信息

Rajati Mohsen, Zarringhalam Mohammad Ali

机构信息

Sinus and Surgical Endoscopic Research Center, Mashhad University of Medical Sciences, Mashhad, Iran.

Departments of Otorhinolaryngology, Mashhad University of Medical Sciences, Mashhad, Iran.

出版信息

Iran J Otorhinolaryngol. 2019 Mar;31(103):115-118.

PMID:30989078
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6449524/
Abstract

INTRODUCTION

Varicella-zoster virus may cause an infectious disease called Ramsay Hunt syndrome. The related symptoms include facial nerve palsy (FNP), otalgia, the vesicular eruptions of the auricle and external auditory canal, less common ocular movement disorder, facial hypoesthesia, myofascial pain, vestibular symptoms, hearing loss, dysphasia, vocal cord paralysis, as well as tongue paralysis due to cranial neuropathies.

CASE REPORT

Herein, we presented the case of a 55-year-old man with left peripheral facial nerve palsy, profound hearing loss, and true vocal cord paralysis. The FNP recovered after 2 weeks and synkinesis totally improved after 4 weeks.

CONCLUSION

Ramsay Hunt syndrome may present as cranial polyneuropathy; therefore, accurate history taking and physical examinations are necessary in this regard. The recovery rate of the vagus nerve is probably fair without polyneuropathy; however, it seems to be poor in cases suffering from polyneuropathy.

摘要

引言

水痘带状疱疹病毒可引发一种名为拉姆齐·亨特综合征的传染病。相关症状包括面神经麻痹(FNP)、耳痛、耳廓和外耳道的水疱性皮疹、较少见的眼球运动障碍、面部感觉减退、肌筋膜疼痛、前庭症状、听力损失、吞咽困难、声带麻痹以及因颅神经病变导致的舌麻痹。

病例报告

在此,我们呈现了一名55岁男性的病例,该患者患有左侧周围性面神经麻痹、重度听力损失和真性声带麻痹。面神经麻痹在2周后恢复,联动在4周后完全改善。

结论

拉姆齐·亨特综合征可能表现为颅多神经病;因此,在这方面进行准确的病史采集和体格检查是必要的。在无多神经病的情况下,迷走神经的恢复率可能尚可;然而,在患有多神经病的病例中,恢复率似乎较差。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3175/6449524/aa773c617163/ijo-31-115-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3175/6449524/e09654e043aa/ijo-31-115-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3175/6449524/b41e00c47c2b/ijo-31-115-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3175/6449524/aa773c617163/ijo-31-115-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3175/6449524/e09654e043aa/ijo-31-115-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3175/6449524/b41e00c47c2b/ijo-31-115-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3175/6449524/aa773c617163/ijo-31-115-g003.jpg

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Ramsay Hunt Syndrome with Multiple Cranial Neuropathy in an Human Immunodeficiency Virus (HIV) Patient.一名人类免疫缺陷病毒(HIV)患者出现伴有多颅神经病变的拉姆齐·亨特综合征。
Am J Case Rep. 2018 Jan 18;19:68-71. doi: 10.12659/ajcr.906834.
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Vocal cord paralysis associated with Ramsay Hunt syndrome: looking back 50 years.
与拉姆齐·亨特综合征相关的声带麻痹:回顾50年
BMJ Case Rep. 2014 Feb 6;2014:bcr2013201038. doi: 10.1136/bcr-2013-201038.
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