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表现为足下垂的全脊髓空洞症。

Holocord syrinx presenting with foot drop.

作者信息

Henderson Duncan, Alix James J P, Sinha Saurabh

机构信息

Neurosurgery, Royal Hallamshire Hospital, Glossop Road, Sheffield S10 2JF, UK.

Neurosurgery, Sheffield Children's Hospital, Clarkson Street, Sheffield S10 2TQ, UK.

出版信息

J Surg Case Rep. 2019 Apr 12;2019(4):rjz082. doi: 10.1093/jscr/rjz082. eCollection 2019 Apr.

DOI:10.1093/jscr/rjz082
PMID:30997008
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6460900/
Abstract

We present an unusual presentation of holocord syrinx. A 4-year-old boy presenting a 2-week history of right sided foot drop. An MRI revealed a holocord secondary to a chiari one malformation. He successfully underwent a craniocervical decompression. Post operatively the syrinx decreased in size and his foot drop completely resolved.

摘要

我们报告了一例罕见的全脊髓空洞症病例。一名4岁男孩,有右侧足下垂2周病史。磁共振成像(MRI)显示全脊髓空洞症继发于Chiari I型畸形。他成功接受了颅颈减压手术。术后,脊髓空洞体积减小,其足下垂完全缓解。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/6460900/66287df25cf4/rjz082f03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/6460900/77de28c333a7/rjz082f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/6460900/815b2a2ebd8b/rjz082f02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/6460900/66287df25cf4/rjz082f03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/6460900/77de28c333a7/rjz082f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/6460900/815b2a2ebd8b/rjz082f02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5476/6460900/66287df25cf4/rjz082f03.jpg

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2
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Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report.一名幼儿因Ⅰ型Chiari畸形合并脑积水和脊髓空洞症导致进行性弛缓性截瘫。病例报告。
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本文引用的文献

1
Chiari malformation type 1 presenting as unilateral progressive foot drop: a case report and review of literature.表现为单侧进行性足下垂的1型Chiari畸形:一例病例报告及文献复习
BMC Pediatr. 2018 Feb 7;18(1):34. doi: 10.1186/s12887-018-1028-8.
2
Rapidly progressive foot drop: an uncommon and underappreciated cause of Chiari I malformation and holocord syrinx.快速进展性足下垂:Chiari I畸形和全脊髓空洞症的一种罕见且未得到充分重视的病因。
BMJ Case Rep. 2013 Jul 29;2013:bcr2013009644. doi: 10.1136/bcr-2013-009644.
3
Holocord syringomyelia presenting as rapidly progressive foot drop.
表现为快速进展性足下垂的全脊髓空洞症。
J Neurosci Rural Pract. 2011 Jul;2(2):195-6. doi: 10.4103/0976-3147.83594.
4
Chiari 1 malformation and holocord syringomyelia presenting as abrupt onset foot drop.表现为急性足下垂的Chiari 1畸形和全脊髓空洞症
Childs Nerv Syst. 2011 Jan;27(1):183-6. doi: 10.1007/s00381-010-1275-y. Epub 2010 Sep 2.
5
Syringomyelia presenting as rapidly progressive foot drop.表现为快速进展性足下垂的脊髓空洞症。
J Clin Neuromuscul Dis. 2002 Mar;3(3):133-4. doi: 10.1097/00131402-200203000-00006.
6
Chiari malformation presenting as a focal motor deficit. Report of two cases.表现为局灶性运动功能缺损的Chiari畸形。两例报告。
J Neurosurg Pediatr. 2008 May;1(5):392-5. doi: 10.3171/PED/2008/1/5/392.
7
Neurological pictures. Chiari I malformation with holocord syrinx.神经影像学图片。伴全脊髓空洞症的Chiari I型畸形。
J Neurol Neurosurg Psychiatry. 2007 Feb;78(2):146. doi: 10.1136/jnnp.2006.099440.