McMillan Hugh J, Sell Erick, Nzau Munyao, Ventureyra Enrique C G
Division of Neurology, Children's Hospital of Eastern Ontario, University of Ottawa, 401 Smyth Road, Ottawa, Ontario, Canada.
Childs Nerv Syst. 2011 Jan;27(1):183-6. doi: 10.1007/s00381-010-1275-y. Epub 2010 Sep 2.
We present two patients with a Chiari 1 malformation and holocord syringomyelia who presented with abrupt onset unilateral foot drop. Neurophysiologic testing was consistent with a proximal nerve root lesion. This assisted with localization and directed magnetic resonance (MR) imaging to lumbosacral spine and nerve roots. Each child underwent a suboccipital craniectomy and laminectomy with duroplasty to decompress the foramen magnum. Each child also showed rapid and complete clinical recovery despite the significant electromyographic and MRI abnormalities on initial study.
我们报告了两名患有Chiari 1畸形和全脊髓空洞症的患者，他们均表现为突发单侧足下垂。神经生理学检查结果与近端神经根病变相符。这有助于定位并指导对腰骶部脊柱和神经根进行磁共振（MR）成像检查。每个孩子都接受了枕下颅骨切除术和椎板切除术并进行硬脑膜成形术，以减压枕骨大孔。尽管初始检查时肌电图和MRI有明显异常，但每个孩子的临床症状均迅速且完全恢复。
