Hasanreisoğlu Murat, Özdemir Hüseyin Baran, Yaylacıoğlu Fulya, Ertop Mestan, Aktaş Zeynep
Gazi University Faculty of Medicine, Department of Ophthalmology, Ankara, Turkey
University of Health Sciences, Ulucanlar Eye Training and Research Hospital, Ophthalmology Clinic, Ankara, Turkey
Turk J Ophthalmol. 2019 Apr 30;49(2):99-101. doi: 10.4274/tjo.galenos.2018.28909.
Relapsing polychondritis is a potentially lethal but rare systemic autoimmune disease. The major site of inflammation is the connective tissue, usually involving the ears, nose, larynx, tracheobronchial tree, and cardiovascular system. Although scleritis and episcleritis are known to be the most probable ocular manifestation, it may also present with uveitis. We present the case of a 22-year-old young lady who initially referred with bilateral red and painful eyes caused by anterior uveitis. Her right ear was also red and painful, consistent with cartilaginous inflammation. She was diagnosed with relapsing polychondritis with bilateral anterior uveitis and chondritis of the ear in conjunction with the rheumatology department. Bilateral anterior uveitis should evaluated and monitored carefully in patients with relapsing polychondritis.
复发性多软骨炎是一种潜在致命但罕见的全身性自身免疫性疾病。炎症的主要部位是结缔组织,通常累及耳朵、鼻子、喉、气管支气管树和心血管系统。虽然巩膜炎和表层巩膜炎是已知最可能的眼部表现,但它也可能表现为葡萄膜炎。我们报告一例22岁年轻女性病例,该患者最初因前葡萄膜炎导致双眼发红、疼痛而就诊。她的右耳也发红、疼痛,符合软骨炎症表现。她被风湿科诊断为复发性多软骨炎伴双侧前葡萄膜炎和耳部软骨炎。对于复发性多软骨炎患者,应仔细评估和监测双侧前葡萄膜炎。