对一名比特蒂结晶状视网膜变性患者进行十年随访的扫频源光学相干断层扫描血管造影术

İpek Şefik Can, Ayhan Ziya, Kadayıfçılar Sibel, Saatci Ali Osman

Dokuz Eylül University Faculty of Medicine, Department of Ophthalmology, İzmir, Turkey

Hacettepe University Faculty of Medicine, Department of Ophthalmology, Ankara, Turkey

Turk J Ophthalmol. 2019 Apr 30;49(2):106-108. doi: 10.4274/tjo.galenos.2018.90768.

A woman with Bietti’s crystalline dystrophy (BCD) was first examined when she was 27 years of age and has been followed for 10 more years. The disease course was monitored initially with spectral domain-optical coherence tomography and then with swept-source optical coherence tomography angiography (OCTA). OCTA analysis showed that choroidal vessels could be visualized at the outer retinal layer segmentation due to retinal pigment epithelial atrophy and blood flow was reduced at the level of choroidal segmentation. OCTA can play a major role in the follow-up of BCD patients by analyzing changes in choroidal flow.

一名患有比埃蒂结晶状营养不良（BCD）的女性在27岁时首次接受检查，并已随访10多年。疾病进程最初通过频域光学相干断层扫描进行监测，随后通过扫频光学相干断层扫描血管造影（OCTA）进行监测。OCTA分析显示，由于视网膜色素上皮萎缩，脉络膜血管可在外层视网膜层分割处显影，脉络膜分割水平的血流减少。通过分析脉络膜血流变化，OCTA在BCD患者的随访中可发挥重要作用。