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一名年轻女性过度宗教信仰伴神经精神症状——排除马基亚法瓦-比尼亚米病。

Overreligious beliefs with neuropsychiatric manifestations in a young lady-Rule out Marchiafava-Bignami disease.

作者信息

Jha Vijoy Kumar, Sharma Dev Prakash, Sharda Vivek, Kumari Abhilasha

机构信息

Classified Specialist (Medicine) and Nephrologist, INHS Kalyani, Vishakapatnam, India.

Classified Specialist (Radiology), INHS Kalyani, Vishakapatnam, India.

出版信息

Med J Armed Forces India. 2019 Apr;75(2):228-231. doi: 10.1016/j.mjafi.2019.02.011. Epub 2019 Apr 15.

DOI:10.1016/j.mjafi.2019.02.011
PMID:31065197
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6495468/
Abstract

Marchiafava- Bignami disease is a rare condition characterized by demyelination of corpus callosum due to alcohol or malnutrition. Here we report a young lady who, due to her religious beliefs had stopped taking food and presented with neuropsychiatric manifestations. Neuroimaging was suggestive of Marchiafava Bignami disease and with adequate nutritional and thiamine therapy she had dramatic improvement clinically and had near complete resolution of lesions in neuroimaging.

摘要

马基亚法瓦-比尼亚米病是一种罕见的疾病,其特征是由于酒精或营养不良导致胼胝体脱髓鞘。在此,我们报告一位年轻女性,她因宗教信仰停止进食,并出现神经精神症状。神经影像学检查提示为马基亚法瓦-比尼亚米病,经过适当的营养和硫胺素治疗,她在临床上有显著改善,神经影像学上的病变几乎完全消退。

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本文引用的文献

1
Neurological and psychiatric findings of marchiafava-bignami disease in a nonalcoholic diabetic patient with high blood glucose levels.一名血糖水平高的非酒精性糖尿病患者的马基亚法瓦-比尼亚米病的神经和精神学表现
J Neuropsychiatry Clin Neurosci. 2015;27(2):e149-50. doi: 10.1176/appi.neuropsych.14030056.
2
Marchiafava-Bignami disease triggered by poorly controlled diabetes mellitus.由控制不佳的糖尿病引发的马基亚法瓦-比尼亚米病。
Neurologia. 2016 Sep;31(7):498-500. doi: 10.1016/j.nrl.2015.01.001. Epub 2015 Feb 26.
3
Diagnosis and management of Marchiafava-Bignami disease: a review of CT/MRI confirmed cases.Marchiafava-Bignami 病的诊断与治疗:CT/MRI 确诊病例回顾。
J Neurol Neurosurg Psychiatry. 2014 Feb;85(2):168-73. doi: 10.1136/jnnp-2013-305979. Epub 2013 Aug 26.
4
Acute Marchiafava-Bignami disease: diffusion-weighted MRI in cortical and callosal involvement.急性马基亚法瓦-比尼亚米病:皮质和胼胝体受累的扩散加权磁共振成像
Yonsei Med J. 2007 Apr 30;48(2):321-4. doi: 10.3349/ymj.2007.48.2.321.
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[Reversible demyelinisation of corpus callosum in the course of Marchiafava-Bignami disease].
Neurol Neurochir Pol. 2006 Mar-Apr;40(2):156-61.
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Clinicoradiologic subtypes of Marchiafava-Bignami disease.马基亚法瓦-比尼亚米病的临床放射学亚型
J Neurol. 2004 Sep;251(9):1050-9. doi: 10.1007/s00415-004-0566-1.