Agati Salvatore, Secinaro Aurelio, Caldaroni Federica, Calvaruso Davide, Manuri Lucia, Gitto Placido, Ferro Giuseppe, Anderson Robert, Vouhè Pascal R, Zanai Rosanna, Campanella Ivana
1 Mediterranean Pediatric Heart Center "Bambino Gesù", Taormina, Italy.
2 Imaging Department-"Bambino Gesù" Pediatric Hospital, Rome, Italy.
World J Pediatr Congenit Heart Surg. 2019 May;10(3):360-363. doi: 10.1177/2150135119829004.
Anomalous origin of a coronary artery from the opposite aortic sinus of Valsalva can present in various ways, ranging from a benign and incidental finding to sudden cardiac death. The variant with an intraseptal subpulmonary course (sometimes referred to as intraconal), is widely perceived to carry a low risk of ischemia and has been considered to be a benign variant, not requiring surgical treatment. In one of our recent patients, however, nuclear scintigraphy highlighted a myocardial perfusion deficit in the territory supplied by the allegedly benign anomalous coronary artery, prompting the need for a more aggressive surgical approach.