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一名51岁男性,伴有肢体刺痛、灼痛及进行性无力。

51-year old man with tingling, burning and progressive limb weakness.

作者信息

Gupta Anu, Kumar Pappula Santhosh, Puri Vinod, Saran Ravindra Kumar, Narang Poonam, Chowdhury Debashish

机构信息

Department of Neurology, Govind Ballabh Pant Institute of Post Graduate Medical Education and Research (GIPMER), New Delhi, India.

Department of Neurology, Max Super Speciality Hospital, New Delhi, India.

出版信息

Pract Neurol. 2018 Oct;18(5):382-388. doi: 10.1136/practneurol-2017-001877. Epub 2018 May 14.

DOI:10.1136/practneurol-2017-001877
PMID:31091191
Abstract

Peripheral neuropathy is a common reason for referral to neurology. Chronic acquired demyelinating neuropathies are an important and varied group with overlapping presentations, and may have an immune-mediated cause. Their correct diagnosis is important as they respond to different treatments; timely intervention can prevent irreversible axonal degeneration. We present a case that highlights the approach to an adult presenting with a chronic demyelinating neuropathy.

摘要

周围神经病变是转诊至神经科的常见原因。慢性获得性脱髓鞘性神经病是一组重要且多样的疾病,临床表现重叠,可能由免疫介导引起。正确诊断这些疾病很重要,因为它们对不同的治疗有反应;及时干预可预防不可逆的轴突变性。我们报告一例病例,以突出对一名患有慢性脱髓鞘性神经病的成年人的诊疗方法。

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Pract Neurol. 2018 Oct;18(5):382-388. doi: 10.1136/practneurol-2017-001877. Epub 2018 May 14.
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