嗜酸性肉芽肿性多血管炎（EGPA）所致的破坏性上气道疾病：首例病例
Destructive Upper Airway Disease from Eosinophilic Granulomatosis with Polyangiitis (EGPA): The Very First Case.
作者信息
Saha Biplab, Saha Aditi, Cordeiro-Rudnisky Fernanda, Shkolnik Boris, Beegle Scott
机构信息
Division of Pulmonary and Critical Care Medicine, Albany Medical Center, Albany, NY, USA.
Department of Medicine, Saint Barnabas Medical Center, Livingston, NJ, USA.
出版信息
Case Rep Rheumatol. 2019 May 23;2019:6173869. doi: 10.1155/2019/6173869. eCollection 2019.
Eosinophilic granulomatosis with polyangiitis (EGPA) is a multisystem vasculitic disorder that predominantly affects medium- and small-sized blood vessels. EGPA belongs to a group of vasculitides known as anti-neutrophil cytoplasmic antibody- (ANCA-) associated vasculitis (AAV). Upper airway involvement is seen in all ANCA-associated vasculitides, but destructive upper airway disease has never been reported in patients with EGPA. We report the first case of erosive chondritis and saddle nose deformity in a 50-year-old patient suffering from EGPA.
嗜酸性肉芽肿性多血管炎（EGPA）是一种多系统血管炎疾病，主要累及中、小血管。EGPA属于一组被称为抗中性粒细胞胞浆抗体（ANCA）相关性血管炎（AAV）的血管炎。上呼吸道受累在所有ANCA相关性血管炎中均可见，但EGPA患者从未有过破坏性上呼吸道疾病的报道。我们报告了首例患有EGPA的50岁患者出现糜烂性软骨炎和鞍鼻畸形的病例。
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