Mantz J, De Brux J L, Pansard Y, Barbier-Bohm G, Desmonts J M, Pernot C, Langlois J
Départment d'Anesthésiologie et Réanimation chirurgicale, hôpital Bichat, Paris.
Arch Mal Coeur Vaiss. 1987 Nov;80(12):1819-22.
We report a case of vagal hypertonia syndrome in a newborn infant, developed after surgical repair of an aortic coarctation combined with banding of the pulmonary artery trunk. The parasympathetic activity had adverse repercussions on haemodynamics. The diagnosis was confirmed by prolonged asystole on the oculocardiac reflex and by concomitant arrhythmia and disorders of conduction demonstrated by Holter recordings. To our knowledge, no other case of vagal hypertonia associated with a congenital cardiopathy has yet been reported. Infants with this syndrome are at a high risk of sudden death. Treatment with vagolytic drugs is of questionable value, and prolonged supervision of the patient is mandatory.
我们报告一例新生儿迷走神经张力亢进综合征，该患儿在主动脉缩窄手术修复并结扎肺动脉干后发病。副交感神经活动对血流动力学产生了不良影响。通过眼心反射时的长时间心搏停止以及动态心电图记录显示的伴随心律失常和传导障碍，确诊了该疾病。据我们所知，尚未有其他与先天性心脏病相关的迷走神经张力亢进病例的报道。患有该综合征的婴儿猝死风险很高。使用抗迷走神经药物治疗的价值存疑，对患者进行长期监测是必要的。
