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普拉德-威利综合征患者的口腔健康:当前观点

Oral health in patients with Prader-Willi syndrome: current perspectives.

作者信息

Bantim Yasmin Comoti Vita, Kussaba Sérgio Takashi, de Carvalho Gilberto Paiva, Garcia-Junior Idelmo Rangel, Roman-Torres Caio Vinícius Gonçalves

机构信息

Department of Surgery an Integrated Clinic, Araçatuba School of Dentistry, São Paulo State - University Unesp, Araçatuba, SP, Brazil.

Department of Dentistry, Cathedral College, Boa Vista, RR, Brazil.

出版信息

Clin Cosmet Investig Dent. 2019 Jul 4;11:163-170. doi: 10.2147/CCIDE.S183981. eCollection 2019.

Abstract

Prader-Willi syndrome (PWS) is a rare complex multisystem disorder and presents several aspects related to dentistry. The purpose of this review is to present current perspectives about oral health in patients with PWS. Delay development, hyperphagia, foamy and highly viscous saliva raise the risk of caries and contribute to tooth wear. Cariogenic foods uncontrolled consumption allows to obesity and dental problems progress worsening systemic disorders. These factors can be controlled. The success in follow-ups with caries free and oral health controlled demonstrate the importance of multidisciplinary team intervention corroborated by support at home from birth to adulthood. Thereby, current perspective on the disease is that there is possibility of proper maintenance of oral health in PWS patients. Guided care interferes positively with the overall well-being and quality of life of the individual with PWS and their family. A multidisciplinary team with a focus on teaching patients and family members will help minimize eventual problems.

摘要

普拉德-威利综合征(PWS)是一种罕见的复杂多系统疾病,存在几个与牙科相关的方面。本综述的目的是介绍关于PWS患者口腔健康的当前观点。发育迟缓、食欲亢进、泡沫状且高度黏稠的唾液会增加龋齿风险并导致牙齿磨损。不受控制地食用致龋食物会导致肥胖,牙齿问题会使全身疾病进一步恶化。这些因素是可以控制的。在实现无龋和口腔健康得到控制的随访中取得的成功表明,多学科团队干预以及从出生到成年在家中的支持的重要性。因此,目前对该疾病的看法是,PWS患者有可能保持良好的口腔健康。有针对性的护理对患有PWS的个体及其家庭的整体幸福感和生活质量有积极影响。一个专注于教导患者及其家庭成员的多学科团队将有助于尽量减少可能出现的问题。

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