Song Ki Un, Nam Ok Hyung, Kim Mi Sun, Choi Sung Chul, Lee Hyo-Seol
Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University, Seoul, Korea.
J Dent Anesth Pain Med. 2015 Dec;15(4):251-255. doi: 10.17245/jdapm.2015.15.4.251. Epub 2015 Dec 31.
Prader-Willi syndrome (PWS) is a rare genetic disorder reported rarely in dentistry. Dental practitioners should know the features of PWS because affected patients have a variety of dental symptoms. The current report describes a case of PWS. An 18-year-old male patient presented with traumatic injuries. Initial emergency treatments were performed under sedation, and further treatments were conducted under general anesthesia. After adequate healing, periodic follow-up and dietary management according to the patient's age and nutritional phase were recommended. Dental management of PWS patients consists of active preventive measures in addition to dietary consultation according to age and nutritional phase.
普拉德-威利综合征（PWS）是一种罕见的遗传性疾病，在牙科领域鲜有报道。牙科从业者应了解PWS的特征，因为受影响的患者有多种牙科症状。本报告描述了一例PWS病例。一名18岁男性患者因外伤就诊。最初的急诊治疗在镇静下进行，进一步治疗则在全身麻醉下进行。伤口充分愈合后，建议根据患者年龄和营养阶段进行定期随访和饮食管理。PWS患者的牙科管理除了根据年龄和营养阶段进行饮食咨询外，还包括积极的预防措施。
