• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

一名患有右位心、房间隔缺损和艾森曼格综合征的年轻患者采用静脉-静脉体外膜肺氧合和心肺移植的治疗

Management of a young patient with dextrocardia, atrial septal defect, and Eisenmenger syndrome with venous-venous extracorporeal membrane oxygenation and heart-lung transplantation.

作者信息

Rajab Taufiek Konrad, Kim Taehoon, Keller Steven, Mallidi Hari

机构信息

Division of Cardiac Surgery, Brigham and Women's Hospital, Boston, Massachusetts.

Division of Pulmonary and Critical Care Medicine, Brigham and Women's Hospital, Boston, Massachusetts.

出版信息

J Card Surg. 2019 Oct;34(10):1114-1116. doi: 10.1111/jocs.14168. Epub 2019 Jul 23.

DOI:10.1111/jocs.14168
PMID:31332841
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7307744/
Abstract

Dextrocardia is a rare congenital condition which presents important challenges for surgical management. We discuss a patient with dextrocardia, atrial septal defect, and Eisenmenger syndrome, which ultimately led to decompensated end-stage lung disease and heart-lung transplant. Venous-venous extracorporeal membrane oxygenation was an important strategy to bridge the patient until donor organs became available. Transplantation of a heart-lung block allowed for the treatment of the patient's underlying congenital heart defect, anatomic reversal of dextrocardia with appropriate venous and arterial connections, and management of pulmonary damage from pulmonary hypertension.

摘要

右位心是一种罕见的先天性疾病,给外科治疗带来了重大挑战。我们讨论了一名患有右位心、房间隔缺损和艾森曼格综合征的患者,该疾病最终导致了失代偿性终末期肺病并进行了心肺移植。静脉-静脉体外膜肺氧合是在供体器官可用之前维持患者生命的重要策略。心肺联合移植能够治疗患者潜在的先天性心脏缺陷,通过适当的动静脉连接实现右位心的解剖学反转,并处理肺动脉高压导致的肺损伤。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af16/7307744/bd12163cf355/nihms-1600102-f0002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af16/7307744/3edd82bd126a/nihms-1600102-f0001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af16/7307744/bd12163cf355/nihms-1600102-f0002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af16/7307744/3edd82bd126a/nihms-1600102-f0001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af16/7307744/bd12163cf355/nihms-1600102-f0002.jpg

相似文献

1
Management of a young patient with dextrocardia, atrial septal defect, and Eisenmenger syndrome with venous-venous extracorporeal membrane oxygenation and heart-lung transplantation.一名患有右位心、房间隔缺损和艾森曼格综合征的年轻患者采用静脉-静脉体外膜肺氧合和心肺移植的治疗
J Card Surg. 2019 Oct;34(10):1114-1116. doi: 10.1111/jocs.14168. Epub 2019 Jul 23.
2
Heart-lung transplantation in situs inversus totalis.全内脏转位患者的心肺移植。
Ann Thorac Surg. 2009 Sep;88(3):1002-3. doi: 10.1016/j.athoracsur.2009.01.060.
3
Not All Septal Defects Are Equal: Outcomes of Bilateral Lung Transplant With Cardiac Defect Repair vs Combined Heart-Lung Transplant in Patients With Eisenmenger Syndrome in the United States.并非所有的间隔缺损都一样:美国 Eisenmenger 综合征患者行心脏缺陷修补的双侧肺移植与心肺联合移植的结局比较。
Chest. 2020 Nov;158(5):2097-2106. doi: 10.1016/j.chest.2020.05.597. Epub 2020 Jun 18.
4
Successful Implementation of Extracorporeal Membrane Oxygenation Support as a Bridge to Heart-Lung Transplantation in an Eisenmenger's Syndrome Patient With Paradoxical Coronary Embolism.在一名患有反常冠状动脉栓塞的艾森曼格综合征患者中成功实施体外膜肺氧合支持作为心肺移植的桥梁
J Investig Med High Impact Case Rep. 2019 Jan-Dec;7:2324709619846575. doi: 10.1177/2324709619846575.
5
Living-donor lobar lung transplantation and closure of atrial septal defect for adult Eisenmenger's syndrome.成人艾森曼格综合征行活体供肺叶移植同期房间隔缺损修补术
J Heart Lung Transplant. 2009 Oct;28(10):1107-9. doi: 10.1016/j.healun.2009.06.021.
6
Backtable ventricular and atrial septal defect repair of an Eisenmenger allograft with concomitant domino heart transplantation.艾森曼格同种异体移植物合并多米诺心脏移植的体外后台室间隔和房间隔缺损修复术。
J Thorac Cardiovasc Surg. 2002 Feb;123(2):374-6. doi: 10.1067/mtc.2002.119062.
7
Management of Eisenmenger syndrome by cardiac defect closure combined bilateral lung transplantation with intraoperative venoarterial ECMO support.心脏缺陷封堵联合双侧肺移植术并术中静脉-动脉体外膜肺氧合支持治疗艾森曼格综合征。
J Card Surg. 2021 Apr;36(4):1560-1562. doi: 10.1111/jocs.15360. Epub 2021 Jan 24.
8
Percutaneous closure of atrial septal defect with situs solitus and dextrocardia.经皮闭合合并右位心的心房隔缺损。
Asian Cardiovasc Thorac Ann. 2015 Feb;23(2):202-5. doi: 10.1177/0218492313500498. Epub 2013 Oct 29.
9
Extracorporeal membrane oxygenation after lung or heart-lung transplantation.肺或心肺移植后的体外膜肺氧合
ASAIO J. 1993 Jul-Sep;39(3):M453-6. doi: 10.1097/00002480-199307000-00060.
10
Single-lung transplantation with atrial septal defect repair for Eisenmenger's syndrome.单肺移植联合房间隔缺损修复术治疗艾森曼格综合征
Ann Thorac Surg. 1991 Aug;52(2):300-3. doi: 10.1016/0003-4975(91)91359-4.

引用本文的文献

1
Extracorporeal life support as rescue therapy in severe bronchiectasis with Kartagener's syndrome.体外生命支持作为卡塔格内综合征所致严重支气管扩张症的挽救治疗方法
Anaesthesiol Intensive Ther. 2022;54(4):334-338. doi: 10.5114/ait.2022.120997.
2
Sinus venosus atrial septal defect and partial anomalous pulmonary venous connection in a patient with dextrocardia.右侧心耳房隔缺损伴部分性肺静脉异位连接于右位心患者。
BMJ Case Rep. 2022 Feb 28;15(2):e245523. doi: 10.1136/bcr-2021-245523.

本文引用的文献

1
Venovenous Extracorporeal Membrane Oxygenation for Acute Respiratory Failure in a Liver Transplant Patient: A Case Report.肝移植患者急性呼吸衰竭的静脉-静脉体外膜肺氧合:一例报告
Transplant Proc. 2018 Dec;50(10):4038-4041. doi: 10.1016/j.transproceed.2018.07.013. Epub 2018 Jul 7.
2
Persistent dextrocardia after adult orthotopic heart transplantation in a patient with complex congenital heart disease.一名患有复杂先天性心脏病的患者在成人原位心脏移植后出现持续性右位心。
J Thorac Cardiovasc Surg. 2019 May;157(5):e271-e273. doi: 10.1016/j.jtcvs.2018.11.019. Epub 2018 Nov 17.
3
Successful heart-lung-kidney and domino heart transplantation following veno-venous extracorporeal membrane oxygenation support.在静脉-静脉体外膜肺氧合支持下成功进行心肺肾联合移植及多米诺心脏移植。
Interact Cardiovasc Thorac Surg. 2019 Feb 1;28(2):316-317. doi: 10.1093/icvts/ivy251.
4
A Weaning Protocol for Venovenous Extracorporeal Membrane Oxygenation With a Review of the Literature.一项关于静脉-静脉体外膜肺氧合的撤机方案及文献综述
Artif Organs. 2018 Jun;42(6):605-610. doi: 10.1111/aor.13087. Epub 2018 Jan 18.
5
Outcomes of lung transplantation for primary ciliary dyskinesia and Kartagener syndrome.原发性纤毛运动障碍和卡塔格内综合征的肺移植结局。
J Heart Lung Transplant. 2016 Nov;35(11):1377-1378. doi: 10.1016/j.healun.2016.08.025. Epub 2016 Sep 7.
6
Insertion of the Avalon cannula for venovenous extracorporeal membrane oxygenation in a patient with an implanted ASD occlusion device.在一名植入房间隔缺损封堵装置的患者中插入Avalon套管进行静脉-静脉体外膜肺氧合。
Heart Surg Forum. 2015 Feb 27;18(1):E031-2. doi: 10.1532/hsf.1225.
7
Heart-lung transplantation in situs inversus totalis.全内脏转位患者的心肺移植。
Ann Thorac Surg. 2009 Sep;88(3):1002-3. doi: 10.1016/j.athoracsur.2009.01.060.
8
Beating heart surgery in a patient with dextrocardia and complete situs inversus.右位心并完全性内脏反位患者的心脏不停跳手术。
J Card Surg. 2003 Mar-Apr;18(2):170-2. doi: 10.1046/j.1540-8191.2003.02008.x.
9
Heart-lung transplantation in situs inversus. A case report in a patient with Kartagener's syndrome.镜面右位心患者的心肺移植。1例患有卡塔格内综合征患者的病例报告。
J Thorac Cardiovasc Surg. 1992 Feb;103(2):307-13.
10
Technique of combined heart-lung transplantation.心肺联合移植技术
J Card Surg. 1992 Dec;7(4):313-23. doi: 10.1111/j.1540-8191.1992.tb01021.x.