Paul Jed M, Orlovich Daniel S, Patton John W, Qian Xiang
From the Department of Anesthesiology, Perioperative and Pain Medicine, Stanford University, Stanford, California.
A A Pract. 2019 Oct 15;13(8):319-321. doi: 10.1213/XAA.0000000000001066.
Pachyonychia congenita (PC) is a rare, inherited disorder of keratin filaments characterized by palmoplantar hyperkeratosis, keratoderma, and extreme pain. Management is largely symptomatic and typically involves multimodal pain control strategies. Here, we report the treatment of one 21-year-old man's refractory neuropathic PC pain with a 4-day inpatient ketamine infusion. Within 1 night of beginning treatment, his pain diminished to a 0/10 without any adverse effects, with effects lasting 2 weeks. No reported PC pain regimens have made use of intravenous ketamine; thus, we suggest recurrent ketamine infusions as an additional option in the multimodal pain regimen for patients with PC.
先天性厚甲症(PC)是一种罕见的遗传性角蛋白丝疾病,其特征为掌跖角化过度、皮肤角化病和剧痛。治疗主要是对症治疗,通常涉及多模式疼痛控制策略。在此,我们报告了一名21岁男性难治性神经性PC疼痛患者接受为期4天的氯胺酮住院静脉输注治疗的情况。在开始治疗的1个晚上内,他的疼痛减轻至0/10,且无任何不良反应,效果持续了2周。既往报道的PC疼痛治疗方案均未使用静脉注射氯胺酮;因此,我们建议重复进行氯胺酮输注,作为PC患者多模式疼痛治疗方案中的一种额外选择。