Nangia Purna, Shah Dhaivat, Saurabh Kumar, Roy Rupak
Department of Vitreo Retina, Aditya Birla Sankara Nethralaya, Kolkata, India.
GMS Ophthalmol Cases. 2019 Jun 18;9:Doc21. doi: 10.3205/oc000110. eCollection 2019.
Pattern dystrophies are a group of inherited disorders of the retinal pigment epithelium. A 44-year-old female came with loss of vision in her right eye. The fundus of both eyes showed flecks in the posterior pole with a CNVM in the right eye. FFA and SD OCT confirmed the presence of CNVM. The patient underwent treatment with anti-VEGF injection. Post treatment, the vision improved with a reduction in subretinal fluid along with a scarring CNVM. To conclude, we report an extremely rare case of PDSFF associated CNVM and its favourable response to anti-VEGF injection.
斑纹状营养不良是一组视网膜色素上皮的遗传性疾病。一名44岁女性因右眼视力丧失前来就诊。双眼眼底后极部可见斑点,右眼有脉络膜新生血管(CNVM)。荧光素眼底血管造影(FFA)和频域光学相干断层扫描(SD OCT)证实了CNVM的存在。该患者接受了抗血管内皮生长因子(VEGF)注射治疗。治疗后,视力改善,视网膜下液减少,同时CNVM形成瘢痕。总之,我们报告了一例极其罕见的与图案状黄斑视网膜病变(PDSFF)相关的CNVM病例及其对抗VEGF注射的良好反应。