Andrade Natália Silva, Tenório Jefferson R, Gallottini Marina
Special Care Center, School of Dentistry, University of São Paulo, São Paulo, São Paulo, Brazil.
School of Dentistry, Special Care Center, University of São Paulo, São Paulo, São Paulo, Brazil.
Spec Care Dentist. 2019 Sep;39(5):538-542. doi: 10.1111/scd.12412. Epub 2019 Jul 30.
Turner syndrome (TS) is a genetic disorder associated with abnormalities of the X-chromosome, occurring in about 1 in 2000 to 1 in 3000 live-born girls. We present a case of a 14-year-old girl with TS, who was referred to our outpatient clinic in 2016 because of an ectopic eruption.
Dental clinical examination and radiographic investigation revealed eight supernumerary teeth, short roots, enamel hypoplasia, increased overjet, rotation and displacement of teeth, moderate gingivitis and morphological alteration of the upper right central incisor. Dental treatment included extraction of erupted supernumerary teeth, composite resin restoration, supragingival scaling and oral hygiene for plaque control.
The unpublished finding of supernumerary teeth in our patient has led us to suggest the investigation of this dental developmental anomaly in other patients with Turner syndrome.
特纳综合征（TS）是一种与X染色体异常相关的遗传性疾病，在每2000至3000名活产女孩中约有1例发生。我们报告一例14岁患特纳综合征的女孩，她于2016年因异位疹被转诊至我们的门诊。
牙科临床检查和影像学检查发现8颗多生牙、牙根短、釉质发育不全、覆盖加大、牙齿旋转和移位、中度牙龈炎以及右上中切牙形态改变。牙科治疗包括拔除已萌出的多生牙、复合树脂修复、龈上洁治以及控制牙菌斑的口腔卫生措施。
我们患者中多生牙这一未发表的发现促使我们建议对其他特纳综合征患者进行这种牙齿发育异常的调查。
