Mauran P, Brévière G M, Rey C, Friedli B, Dupuis C
Service de cardiologie infantile, hôpital cardiologique, Lille.
Arch Mal Coeur Vaiss. 1988 May;81(5):649-53.
The association of a restrictive ventricular septal defect with a pulmonary tract obstruction is rare and may cause diagnostic and therapeutic problems. The authors report their experience of such an association in 10 children. 3 had a tetralogy of Fallot (1 death), 4 a double-outlet right ventricle (2 deaths), and 3 a coarctation of the aorta with ventricular septal defect and pulmonary artery banding (no death). Prognosis depends on the type of malformation. It has improved with years because of sooner recognition of these malformations and better surgical technics and post-operative care.
限制性室间隔缺损合并肺动脉梗阻较为罕见,可能会导致诊断和治疗方面的问题。作者报告了他们对10例此类患儿的治疗经验。其中3例为法洛四联症(1例死亡),4例为右心室双出口(2例死亡),3例为主动脉缩窄合并室间隔缺损及肺动脉束带术(无死亡病例)。预后取决于畸形的类型。由于对这些畸形的更早识别、更好的手术技术和术后护理,其预后情况多年来有所改善。