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华氏巨球蛋白血症的诊断

Diagnosis of Waldenström macroglobulinemia.

作者信息

Smith Tyler, Wong Mitchell, Goldson Tove M, Forjuoh Samuel N

机构信息

Department of Family and Community Medicine, Baylor Scott & White Health, and College of Medicine, Texas A&M Health Science CenterTempleTexas.

出版信息

Proc (Bayl Univ Med Cent). 2019 May 21;32(3):394-396. doi: 10.1080/08998280.2019.1596681. eCollection 2019 Jul.

Abstract

Waldenström macroglobulinemia is a rare disorder affecting about 1400 people annually in the United States. This case report reviews from a primary care provider's perspective the initial presentation of a patient who complained of fatigue and dizziness that ultimately led to hospital admission with a diagnosis of Waldenström macroglobulinemia. The referral to hematology/oncology prompting the bone marrow biopsy that led to the diagnosis highlights the important role of the primary care provider in the initial workup, coordination among specialists, and overall management of patients with rare disorders.

摘要

华氏巨球蛋白血症是一种罕见疾病,在美国每年约有1400人受其影响。本病例报告从初级保健提供者的角度回顾了一名患者的初始表现,该患者主诉疲劳和头晕,最终因华氏巨球蛋白血症诊断入院。促使进行骨髓活检从而确诊的血液学/肿瘤学转诊,凸显了初级保健提供者在罕见疾病患者初始检查、专家间协调及整体管理中的重要作用。

相似文献

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Diagnosis of Waldenström macroglobulinemia.华氏巨球蛋白血症的诊断
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Initial Evaluation of the Patient with Waldenström Macroglobulinemia.华氏巨球蛋白血症患者的初始评估
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本文引用的文献

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IgG lymphoplasmacytic lymphoma: a case report.IgG 淋巴浆细胞淋巴瘤:一例报告
Ann Biol Clin (Paris). 2018 Dec 1;76(6):665-668. doi: 10.1684/abc.2018.1384.
2
Initial Evaluation of the Patient with Waldenström Macroglobulinemia.华氏巨球蛋白血症患者的初始评估
Hematol Oncol Clin North Am. 2018 Oct;32(5):811-820. doi: 10.1016/j.hoc.2018.05.008. Epub 2018 Jul 23.
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Chronic diarrhea: A case of Waldenström macroglobulinemia.慢性腹泻:一例华氏巨球蛋白血症病例。
Rev Gastroenterol Mex (Engl Ed). 2018 Oct-Dec;83(4):467-469. doi: 10.1016/j.rgmx.2017.08.003. Epub 2018 Feb 17.
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Waldenstrom's Macroglobulinemia: An Update.华氏巨球蛋白血症:最新进展
Mediterr J Hematol Infect Dis. 2018 Jan 1;10(1):e2018004. doi: 10.4084/MJHID.2018.004. eCollection 2018.
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International prognostic scoring system for Waldenstrom macroglobulinemia.华氏巨球蛋白血症国际预后评分系统。
Blood. 2009 Apr 30;113(18):4163-70. doi: 10.1182/blood-2008-08-174961. Epub 2009 Feb 5.

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