Isaeva N V, Prokopenko S V, Rodikov M V, Abroskina M V, Ondar V S, Subocheva S A, Ippolitova E V, Kuznetsov V Yu
Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk, Russia; Regional Clinical Hospital, Krasnoyarsk, Russia.
Voino-Yasenetsky Krasnoyarsk State Medical University, Krasnoyarsk, Russia.
Zh Nevrol Psikhiatr Im S S Korsakova. 2019;119(6):96-100. doi: 10.17116/jnevro201911906196.
Stiff-person syndrome (SPS) is a rare chronic neurological disease characterized by progressing muscle rigidity and painful muscle spasms. The signs of SPS are pain and stiffness in spinal, abdominal and cervical muscles, increased muscle tonus in extensor muscles of extremities, constant stiffness of paravertebral and abdominal muscles and muscle spasms. A clinical case of a SPS patient T., aged 23 years, is presented. The peculiarity of this case is additional left-sided peripheral upper extremity monoparesis, which is most likely associated with the development of left-sided compression-ischemic brachial plexopathy resulted from profound muscular tonic syndrome in the neck and shoulder girdles.
僵人综合征（SPS）是一种罕见的慢性神经疾病，其特征为进行性肌肉僵硬和疼痛性肌肉痉挛。SPS的症状包括脊柱、腹部和颈部肌肉疼痛和僵硬，四肢伸肌肌张力增加，椎旁和腹部肌肉持续僵硬以及肌肉痉挛。本文介绍了一例23岁的SPS患者T.的临床病例。该病例的特殊之处在于额外出现了左侧上肢周围性单瘫，这很可能与颈部和肩胛带严重肌肉强直性综合征导致的左侧压迫性缺血性臂丛神经病变有关。
