Kotov A S, Dolgova S G, Bunak M S, Abramenko A S, Stashuk G A, Borodin A V, Tokareva Yu V, Mukhina E V
Moscow Regional Research and Clinical Institute, Moscow, Russia.
Zh Nevrol Psikhiatr Im S S Korsakova. 2019;119(6):107-112. doi: 10.17116/jnevro2019119061107.
Balo's concentric sclerosis (BCS) is a rare demyelinating disease, first described by Hungarian neurologist Josef Balo in 1928. BCS occurs predominantly in young adults, the average age of onset of the disease - 34 years (range from 3 to 62 years). Our case report describes a 27-year woman with acute onset progressive right-side pyramidal weakness, MRI results showed a variant of demyelination as Balo's concentric sclerosis.
巴洛同心圆性硬化(BCS)是一种罕见的脱髓鞘疾病,由匈牙利神经学家约瑟夫·巴洛于1928年首次描述。BCS主要发生于年轻人,该病的平均发病年龄为34岁(范围为3至62岁)。我们的病例报告描述了一名27岁女性,急性起病,右侧锥体束进行性无力,磁共振成像(MRI)结果显示为巴洛同心圆性硬化的脱髓鞘变异型。