Funderburk S J, Barrett C T, Klisak I
Ann Genet. 1978 Dec;21(4):219-22.
This report describes an infant with fatal congenital heart disease, cleft palate, brain malformations, and trisomy 8p resultant from the paternal balanced reciprocal translocation, rcp(8;15) (p11;p11). Review of six previously reported trisomy 8p patients (resultant from parental balanced translocation in each instance) revealed severe mental retardation in five, short stature in all, and a variety of brain, skeletal, and cardiac defects. The features of the seven trisomy 8p patients reviewed here are not sufficiently similar to suggest a distinct dysmorphic syndrome. In addition the features differ from those in the trisomy 8 mosaicism syndrome, in which the mental retardation and malformations are generally less severe.
本报告描述了一名患有致命性先天性心脏病、腭裂、脑畸形以及因父亲平衡易位rcp(8;15)(p11;p11)导致的8p三体综合征的婴儿。对先前报道的6例8p三体综合征患者(均由父母平衡易位导致)的回顾显示,5例有严重智力发育迟缓,所有患者均身材矮小,且存在各种脑、骨骼和心脏缺陷。本文回顾的7例8p三体综合征患者的特征并不十分相似,无法提示一种独特的畸形综合征。此外,这些特征与8号染色体三体嵌合综合征不同,后者的智力发育迟缓和畸形通常不太严重。